Susac syndrome is a rare microangiopathy of indeterminate etiology, presumably autoimmune, characterized by a triad of encephalopathy, sensorineural hearing loss, and branch retinal artery occlusions occurring predominantly in women. The onset and progression patterns are multiple, mainly of three modes. Fulminant evolution is exceptional, rarely reported across literature. We report through this case a Susac syndrome in a young man in whom evolution was fatal. Magnetic resonance imaging is essential to raise the diagnosis and for follow-up, with almost pathognomonic findings, all the more useful as the clinical triad is usually incomplete and as the encephalopathy is the most limiting of the symptoms.
The issue of the assessment of the contribution of the information systems to performance (IS) is an area of investigation which has been explored a little in Morocco. From an academic point of view, it is a matter of going further into the field of investigation by the enrichment of previous studies on the issue of the alignment of IS and the performance of organizations. From a practical point of view, it meets the expectations of businesses by providing answers to the question of contribution of IS in obtaining high-performance results. Based on the model of strategic alignment, a qualitative study of the exploratory character of hybrid type was conducted with thirteen Moroccan companies of different sizes and operating managers in different sectors of activities. This is in a bid to assess the applicability of research including the relevance and inadequacies of constructs in the field. The results of this study allowed us to adapt our research hypotheses to the Moroccan context. As a result, a number of variables have been integrated. These makes it possible to build our final alignment of IS model and phase confirmatory.
Aims: The chondromyxoid tumor is a benign primary bone tumor of cartilaginous differentiation whose location is atypical and rarely described in the literature.
Case Report: A 10 year old child, who consulted the emergency room of the children's hospital of Rabat for a hard and painful swelling of the right iliac fossa, rapidly increasing in volume. Biological tests were normal. The radiography showed a mixed lytic and condensing lesion, heterogeneous, of the right iliac wing, prompting an magnetic resonance imaging (MRI).
Discussion: Chondromyxoid fibroma usually affects young subjects and manifests clinically as pain and swelling. Pathological fractures are common.
On standard radiography, in long bones, there is an eccentric geographic gap, blowing out the cortex. On flat bones such as the iliac bone, the tumor is often polycyclic and mixed, combining condensation and bone lysis. Intratumoral microcalcifications may be encountered.
MRI is the key examination to evoke the diagnosis of chondromyxoid fibroma.
Conclusion: Imaging and in particular MRI plays multiple and fundamental roles in the management of chondromyxoid fibroma. MRI provides diagnostic guidance, particularly in the case of atypical localization.
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