Rationale:Esophageal achalasia is characterized by impaired relaxation of the cardia and dilation of the intrathoracic part of the esophagus. We describe the late presentation of achalasia in an 11-year old girl.Patient concerns:She suffered from recurrent pneumonia, obstructive bronchitis, and problems with swallowing solid food. Her family noted a wet pillow in the morning.Diagnoses:This case report describes the typical symptoms of achalasia in children in order to facilitate earlier diagnosis of this rare disease. Our patient was admitted to a pediatric hospital for treatment of severe pneumonia, low-grade fever, and pancreatitis. A computed tomography (CT) scan of the thorax showed massive dilation of the esophagus and infiltration and partial atelectasis of the right lung. An upper gastrointestinal contrast study confirmed massive dilation of the esophagus and stenosis at the level of the cardia.Interventions:We performed laparoscopic Heller myotomy combined with Dor fundoplication. Bronchoscopic lavages were conducted in the pre- and postoperative period to relief obstruction of bronchi by purulent mucus secretions.Outcomes:A further upper gastrointestinal contrast study demonstrated patency of the cardia and fast propulsive movement of contrast agent into the stomach. At follow up 2 months after the operation, the girl had gained 3 kg of body weight, and her respiratory, gastrointestinal, and swallowing symptoms had subsided. At follow-up 12 months after the operation, no recurrent symptoms of achalasia were recorded.Lessons:Late presentation of achalasia in children can mimic respiratory and gastrointestinal diseases. Laparoscopic Heller myotomy combined with Dor fundoplication is feasible and advisable in children suffering from achalasia of the cardia.

Представлено редкое клиническое наблюдение декомпенсированного приобретенного стеноза привратника у ребенка четырех лет. Показана возможность выполнения лапароскопической резекции желудка у пациента младшего возраста. Отмечено полное отсутствие ранних и поздних послеоперационных осложнений, достигнуты отличные функциональный и косметический результаты проведенного лечения. Ключевые слова: приобретенный стеноз привратника, ребенок младшего возраста, лапароскопическая резекция желудка

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After clinical and neurophysiological examinations of 22 patients with developmental anomalies of the rectum and anus, who suffered of fecal incontinence of type III and who were operated in the Vladimirsky Moscow Region Clinical Institute, a modern approach to the diagnostics of neuromuscular disorders has been proposed. A particular attention was paid to the sacral plexus and its branches. A detailed examination of the sexual nerve and its functions was made using a St. Mark disposable rectal electrode. The optimal evaluation of motor potentials from the thigh muscles under transrectal stimulation of the sacral plexus was made; findings of EMG diagnostics were compared too. The researchers backgrounded an optimal modality for treating this pathology: not only surgical tactics, but also patient’s reserve capabilities in restoring lost functions using EMG biological feedback.