A Case of Late Presenting Unicuspid Aortic Valve in a 62‐Year‐Old Female

Chester, Rebecca; Sahni, Sheila; Huynh, Tracy

doi:10.1111/echo.12881

Cited by 5 publications

(7 citation statements)

References 8 publications

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“…UAV has more early, more accelerated, more severe valvular calcification as well as a smaller orifice than BAV or TAV, which would lead to more early, more accelerated and more severe AS in UAV than in BAV or TAV [32][33][34]. Likewise, UAV patients present associated clinical symptoms of AS at earlier age and progress faster [4,8,35]. Also, the irregularly deposited calcific spurs may prevent the cusp from closing the orifice, thus AR may occur [1].…”

Section: Valvular Function and Clinical Presentationmentioning

confidence: 99%

“…The unicommissural form appears to have a less-aggressive course. It usually develops symptoms until adulthood since the formation of a commissure brings a relatively larger valvular orifice area compared to acommissural type [4, 5, 8, 12, 35, 39, 40]. Moreover, the valvular lesion would progress further with the aging, the accelerated leaflet calcification and fibrosis resulted from the aortic valve malformation [13, 38, 41].…”

Section: Valvular Function and Clinical Presentationmentioning

confidence: 99%

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Unicuspid Aortic Valve: A Rare Congenital Anomaly

Jian-Hong¹

2021

Cardiology

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Unicuspid aortic valve (UAV) is a rare congenital aortic valve anomaly. It has two subtypes and often is associated with aortic valve dysfunction and corresponding clinical presentations. Echocardiography is the first choice of diagnostic method for UAV. Three-dimensional echocardiography has played an increasingly important role in diagnosis, intraprocedural guidance, and post-procedural assessment in recent years. There remain challenges in distinguishing UAV from bicuspid aortic valve (BAV) or tricuspid aortic valve (TAV). Misdiagnosis is most resulted from raphes or leaflet calcifications. Multi-modality imaging has obvious advantages over single-modality imaging and is crucial for UAV diagnosis. Accurate identification of aortic valve morphology is important to choose the best treatment. Aortic balloon valvoplasty, surgical valvotomy, commissurotomy, Ross procedure, surgical valve repair and surgical replacement are most common treatment modalities of UAV. In this review, we aim to discuss UAV including epidemiology, definition, classification, diagnostic importance and necessity, valvular function, clinical presentation, associated disorders, non-invasive diagnostic modalities and therapeutic approaches.

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Section: Valvular Function and Clinical Presentationmentioning

confidence: 99%

Section: Valvular Function and Clinical Presentationmentioning

confidence: 99%

Unicuspid Aortic Valve: A Rare Congenital Anomaly

Jian-Hong¹

2021

Cardiology

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“…During embryonic development, the AV is formed from three tubercles; abnormal fusion of which can result in either a UAV or a BAV [9]. UAV incidence has been estimated to be only 0.02% in the general population [10,11], but it remains a frequent reason for AV operation in teenagers or young adults younger than 25 years [12,13].…”

mentioning

confidence: 99%

“…The typical age of patients presenting with a symptomatic UAV is from their early 30s to their 60s [5,14], which is 10 to 20 years earlier than for patients with BAV [5,13,[15][16][17].…”

mentioning

confidence: 99%

Aortic Valve Repair of a Stenotic Unicuspid Aortic Valve in Young Patients

Kolesár

Toporcer

Bajmoczi

et al. 2018

The Annals of Thoracic Surgery

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“…Unicuspid aortic valve is rare in adults, with an estimated incidence of 0.02% in a referral population. Patients with UAV mostly present with aortic stenosis, because UAV was usually heavily calcified, and the cusp was rigid.…”

mentioning

confidence: 99%

Severe Aortic Regurgitation Caused by Unicuspid Aortic Valve Based on Quadricuspid Aortic Valve

et al. 2015

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A 41-year-old man was admitted to our hospital because of progressive shortness of breath.Two-dimensional transthoracic echocardiography (2DTTE) revealed that the end-diastolic and end-systolic diameters of the left ventricle were 61 and 41 mm, respectively, and the left ventricular ejection fraction was 57%, while severe aortic regurgitation (AR) was also observed (Fig. 1A, movie clip S1). Twodimensional transesophageal echocardiography (2DTEE) revealed the presence of a horseshoeshaped unicuspid aortic valve (UAV) with two raphes at 4 and 8 o'clock positions of the aortic leaflet, and prolapse of the noncoronary cusp ( Fig. 1B and C, movie clip S2). In addition, three-dimensional transesophageal echocardiography (3DTEE) clearly showed UAV, and another raphe was observed at the 7 o'clock position of the aortic leaflet ( Fig. 1D and E, movie clip S3). The Bentall procedure was performed, and surgical inspection confirmed the diagnosis of UAV in this case is based on the detection Figure 1. A. 2DTEE shows severe AR. B. 2DTTE shows a horseshoe-shaped unicuspid aortic valve with two raphes at 4 and 8 o'clock positions of the aortic leaflet. C. 2DTEE shows prolapse of the noncoronary cusp (white arrow).

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A Case of Late Presenting Unicuspid Aortic Valve in a 62‐Year‐Old Female

Cited by 5 publications

References 8 publications

Unicuspid Aortic Valve: A Rare Congenital Anomaly

Unicuspid Aortic Valve: A Rare Congenital Anomaly

Aortic Valve Repair of a Stenotic Unicuspid Aortic Valve in Young Patients

Severe Aortic Regurgitation Caused by Unicuspid Aortic Valve Based on Quadricuspid Aortic Valve

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