Background: Hemangioma is one of the umbilical cord anomalies and it is arising from the remnants of embryo hemangioblasts. It is associated with increased perinatal morbidity and mortality.
Case report: We describe an umbilical cord hemangioma that was identified in antenatal period. The patient was referred to our hospital for further evaluation of omphalocele that was noticed at gestational age of 29 week. The mass, measured 80*75*50 mm diameter, was surrounded by edema of the Wharton jelly. Color Doppler imaging revealed arterial and venous flow within the mass. The neoplasm was composed of organized and non-organized capillary vessels within the myxoid stroma. Neoplasm was covered with squamous epithelium focally but the epithelium was widely eroded. The immunohistochemical examination positive staining was obtained for vimentin, desmin, CD34 and SMA.
Conclusion: Umbilical cord anomalies are rare. Early detection and close follow-up can reduce the risk of perinatal morbidity and mortality.