A Rare Type of Double Aortic Arch Diagnosed by Echocardiography in an Asymptomatic 9-Year-Old Patient

Abstract

A case of double aortic arch with an atretic left arch distal to the origin of the left subclavian artery was suspected by echocardiography (ECHO) in an asymptomatic 9-year-old girl and confirmed by magnetic resonance imaging (MRI). The authors report their ECHO findings, which could be an important diagnostic tool for symptomatic patients because confusion exists in the literature regarding the differentiation of the aforementioned rare malformation from a right arch with mirror image branching. The authors support their ECHO proposal with an explanation based on the hypothetical double aortic arch plan set by Edwards.

Incomplete Double Aortic Arch and Window Patent Ductus Arteriosus in a CHARGE Syndrome Patient: A Case Report and Review of Literature

“…2) (Movie 2, supplementary data) imaging was consistent with a DAA [17]. Typically the terminology of an incomplete DAA refers to an atresia of one of the AA resulting in a vascular ring created by the persistent ligamentum of the atretic segment; this entity is rare but described [25][26][27][28]. In our patient, there is no vascular ring as the left dorsal aorta distal to the LSCA completely involuted as confirmed in surgery.…”