Abdominal Aortic Coarctation, Renovascular, Hypertension, and Neurofibromatosis

Mid-Aortic Syndrome and Renovascular Hypertension in a 14-Year-Old Iraqi Girl: Pitfalls in Diagnosis and Surgical Management

“…3,4 Such longitudinal studies have led to universal acceptance that surgical correction of the associated renovascular hypertension is necessary. Rarely, abdominal aortic coarctation has been associated with other uncommon conditions including neurofibromatosis 5,6 and tuberous sclerosis 7 as well as with William's syndrome, a rare congential malformation associated with chromosomal deletion.…”

“…To treat the hypertension and improve renal function, the following bypasses have been utilized: hepatorenal bypass; patch aortoplasty; splenorenal bypass; resection of the hypoplastic aorta with interposition graft; extraanatomic axillo-femoral bypass with Dacron; and bypass with aortic homograft, internal iliac artery, or saphenous vein grafts. 1,5,[11][12][13] Ultimately, more logical and durable surgeries have prevailed as medical technology and an understanding of the natural course of this disease has improved. Presently, surgical bypass with PTFE, renal autotransplantation, and endovascular techniques including angioplasty have emerged as potential first-line treatment options.…”

Renal autotransplantation for the treatment of renovascular hypertension in the pediatric population

“…The less frequent causes of pediatric RVD are middle aortic syndrome [5,17] neurofibromatosis type I [18,19] and extrinsic vascular compression. Children with the first 2 pathologies constitute a selected group of patients due to particular characteristics of their renal arteries or due to ostial localization of RVD and the presence of tough fibrotic tissue refractory to dilation [3,4,20].…”

An Unusual Cause of Young Hypertension

“…The prevalence of asymptomatic disease is unknown. 4 These lesions are progressive in nature. Analysis of the few reported case series revealed that this form of vasculopathy predominantly affects males and presents in the fi rst or second decade.…”