Adrenal ganglioneuroma

Çelik, Varol; Ünal, Gülin Terek; Özgültekin, Recep; Göksel, Süha; Unal, Hilal; Çerçel, Ali

doi:10.1002/bjs.1800830237

Cited by 12 publications

(1 citation statement)

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“…Ganglioneuroma originates from cells of the neural crest that include the sympathetic ganglia and adrenal medulla and hence is related to pheochromocytoma and neuroblastoma (3). The exact incidence of GNs is not known and the median age at diagnosis is approximately 7 years, with a slight female predominance which is consistent with our patient(5). Neuroblastomas occur more frequently than GNs, although both these tumors occur in the same anatomic location, posterior mediastinum (41.5%), retroperitoneum (37.5%), adrenal gland (21%), and neck (8%) (6).…”

Section: Discussionsupporting

confidence: 90%

Anesthesia management of a ganglioneuroma with seizures presenting as pheochromocytoma

Batra¹,

Rajeev²,

Rao

2006

Pediatric Anesthesia

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Ganglioneuromas (GN) are neural crest cell-derived tumors which may coexist with pheochromocytomas, secrete various neuropeptides or the symptoms may mimic that of a pheochromocytoma, producing hypertension or a hypotensive crisis during anesthesia for these tumors. We report here the case of a 7-year-old female child with an adrenal tumor suspected to be a pheochromocytoma, later confirmed by histology as a GN. This child presented with episodic headache, anxiety, palpitations and 3D helical (spiral) computed tomography of the abdomen revealed an adrenal tumor. In addition, the child was diagnosed to have a seizure disorder. She was managed as a pheochromocytoma. Although the child's preoperative catecholamine levels were normal, tumor manipulation caused a hypertensive crisis. We discuss the clinical characteristics of this unusual case, anesthesia management, and the postoperative course.

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Section: Discussionsupporting

confidence: 90%