Aggressive angiomyxoma of broad ligament: an uncommon mesenchymal tumor

Abstract

Aggressive angiomyxoma is a rare mesenchymal tumor occurring predominantly in the pelviperineal region. Authors present a case of a 70 years female presented with history of distention of lower abdomen with recurrent pain since 6 months. On clinical examination there was suspicion of fibroid. On USG it was reported as huge fleshy, soft tissue mass measuring 20x10x9 cm in lower abdominal flanks and pelvis with vascular pedicle attached to right parametrium. Pan-hysterectomy was performed. Right broad ligament showed mass measuring 18.5x10x6 cm. On histopathological examination it was diagnosed as a case of Aggressive angiomyxoma of broad ligament. We are presenting this case for its extreme rarity, clinicohisto-pathological and radiological findings.

A rare case report of a myxoid liposarcoma arising from the broad ligament

“…The aggressive angiomyxoma is distinguished by its extensive vasculature and lack of discernible lipoblasts and its positivity for Desmin and estrogen receptors. 11 Although it has little impact on MLPS diagnosis, immunohistochemistry may help distinguish high-grade MLPS from other round cell sarcomas. Preoperative chemotherapy or radiotherapy frequently results in a significant decrease in cellularity, with only scattered ovoid cells, significant stromal hyalinization, and sometimes maturation into white adipose tissue.…”

“…The aggressive angiomyxoma is distinguished by its extensive vasculature and lack of discernible lipoblasts and its positivity for Desmin and estrogen receptors. 11 …”