Aggressive desmoid fibromatosis: First case in a Rwandan child

Kanyamuhunga, Aimable; McCall, Natalie; Tuyisenge, Lisine; Mumena, Crispus; Stefan, Daniela Cristina

doi:10.7196/sajch.593

Cited by 3 publications

(3 citation statements)

References 5 publications

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“…They can occur in any part of the body [ 12 ] and can be either slow-growing or aggressive forms. The slow-growing tumors are not associated with familial adenomatous polyposis (FAP) and are typically sporadic, while the aggressive ones are typically associated with FAP [ 13 ]. The slow-growing tumors commonly occur in the shoulder girdle or the abdominal wall, with the latter more common in young females during pregnancy or within the first year after childbirth [ 14 , 15 ], as in our patient, although she is nullipara.…”

Section: Discussionmentioning

confidence: 99%

Giant desmoid tumour mimicking recurrent uterine myoma in a nulliparous young Nigerian: a case report

Njoku

Umezurike

2022

J Med Case Reports

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Background Desmoid tumors are rare lesions. Although they demonstrate tumor characteristics, such as infiltrative growth and tendency towards local recurrence, they lack the ability to metastasize. To date, the cause of desmoid tumors is unknown. They can occur in both sexes, but predominant slightly in women, including nulliparous women, of reproductive age, but mostly during and after pregnancy. Case presentation A 36-year-old nulliparous Nigerian woman presented with a large desmoid tumor of the anterior abdominal wall, mimicking recurrent leiomyoma. At presentation, she had a painless abdominal mass for 1 year, which was first noticeable as a small induration that progressively increased in size. The patient had a previous surgical history of open myomectomy for symptomatic fibroids of 3 years duration, prior to presentation. Treatment comprised a complete excision of the tumor with a wide margin and partial omentectomy and the anterior abdominal wall closed in layers, though without prosthesis. The patient subsequently developed incisional hernia. Conclusions Large desmoid tumors may be misdiagnosed or mistaken for uterine leiomyoma or other abdominal or pelvic tumors. Attention should therefore be paid to detailed patient history and systematic clinical evaluation. To guard against incisional hernia associated with surgical resection of huge desmoid tumors, mesh reconstruction is recommended.

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Section: Discussionmentioning

confidence: 99%

Giant desmoid tumour mimicking recurrent uterine myoma in a nulliparous young Nigerian: a case report

Njoku

Umezurike

2022

J Med Case Reports

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“…The slow-growing type is usually sporadic and not associated with FAP. [ 8 ] The slow-growing ones occur commonly in the shoulder girdle or the abdominal wall. The abdominal wall desmoid fibromatosis, like the one found in our patient, is more common in young females either during pregnancy or within the 1 st year of childbirth.…”

Section: Discussionmentioning

confidence: 99%

“…[ 7 ] The use of chemotherapy, radiotherapy, and hormone therapy is controversial and limited to the unresectable tumors. [ 8 ]…”

Section: Introductionmentioning

confidence: 99%

Desmoid Fibromatosis of the Lower Abdominal Wall in Irrua Nigeria

Awe

Eluehike

2018

Niger J Surg

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Desmoid fibromatosis (desmoid tumors) is rare tumors. It can occur as intra-abdominal, extraabdominal, or abdominal wall tumor depending on the site. The abdominal wall type is usually sporadic, but few have been associated with familial adenomatous polyposis. They are commonly seen in young females who are pregnant with a history of the previous cesarean section scar or within the 1st year of the last childbirth. There is an association between this tumor, presence of estrogen receptors, and abdominal trauma. We present a 29-year-old Nigerian woman with fungating lower abdominal wall tumor. This tumor is rare, a high index of suspicion will be very important in making the diagnosis.

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Extra-Abdominal Musculo-Aponeurotic Fibromatosis: A Case with Metachronous Multicentric Lesions of the Right Thigh

Popovska

Betova

Petrov

2014

Journal of Biomedical and Clinical Research

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Fibromatoses are a group of benign proliferations of fibrous tissue with clinical behaviour ranging from that of truly malignant tumours to that of benign reactive fibrous proliferations. Some of the superficial fibromatoses are fairly common but deep ones, also known as desmoid tumours or musculoaponeurotic fibromatoses, are rare. We describe a case of extra-abdominal musculo- aponeurotic fibromatosis in a 22-years old male. He underwent 14 operations for a period of 9 years for fibromatosis of the posterior surface of the right lower limb. The histological findings of the lesions were similar consistent across surgeries and consistent with a diagnosis of aggressive extra-abdominal fibromatosis.

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Aggressive desmoid fibromatosis: First case in a Rwandan child

Cited by 3 publications

References 5 publications

Giant desmoid tumour mimicking recurrent uterine myoma in a nulliparous young Nigerian: a case report

Giant desmoid tumour mimicking recurrent uterine myoma in a nulliparous young Nigerian: a case report

Desmoid Fibromatosis of the Lower Abdominal Wall in Irrua Nigeria

Extra-Abdominal Musculo-Aponeurotic Fibromatosis: A Case with Metachronous Multicentric Lesions of the Right Thigh

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