Alternative rehabilitation treatment for a patient with ectodermal dysplasia

Valle, Daniella Della; Chevitarese, Ana Beatriz Alonso; Maia, Lucianne Cople; Farinhas, João Alfredo

doi:10.17796/jcpd.28.2.55021560w701h2r2

Cited by 12 publications

(11 citation statements)

References 4 publications

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“…Treatment complexity is directly related to patient age and degree of severity 5,14) . In children, the most conservative treatment approach is to wait for completion of skeletal and dental growth before formulating an implant-based prosthetic treatment plan 2) .…”

Section: Discussionmentioning

confidence: 99%

“…So far, at 4 years postoperatively, all the implants continue to show favorable positioning and osseointegration. Regular postoperative follow-up visits are essential in young patients with ED, as the prostheses must be changed in line with new growth and development 5) . The present patient came in for such examinations every 6 months over a 4-year period, during which time the maxillary complete dentures were changed twice and the implant supported prosthesis given occlusal adjustments.…”

Section: Discussionmentioning

confidence: 99%

“…This rare syndrome affects approximately one in 100,000 live births, with the proportion of male to female at five to one. Generally, it is manifested in males, but transmitted by females 5) . The most common oral manifestations are hypo-or anodontia of both the primary and permanent dentition; teeth with morphological (conoid, sharp incisors, molars with a small crown diameter) or developmental anomalies (enamel hypoplasia); and compromised development of alveolar bone, resulting in a reduction in the vertical dimension, which gives the patient a senile appearance 17,18) .…”

Section: Introductionmentioning

confidence: 99%

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Implant-supported Oral Rehabilitation in Child with Ectodermal Dysplasia — 4-year Follow-up

Triches

Ximenes

Souza

et al. 2017

Bull. Tokyo Dent. Coll.

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Ectodermal dysplasia (ED) is an anomaly determined by genetic factors that alter ectodermal structures such as skin, hair, nails, glands, and teeth. Children affected by this condition require extensive, comprehensive, and multidisciplinary treatment. An 8-yearold female patient visited the Dentistry Clinic of the Federal University of Santa Catarina with the chief complaint of multiple missing teeth. The mother reported that the patient had ED. Clinical and radiographic examination revealed the congenital absence of several primary and permanent teeth and tooth germs. Subsequent oral rehabilitation comprised the application of a maxillary denture and mandibular implant-supported fixed prosthesis. The child was also supplied with a wig for further enhancement of esthetics aimed at improving her emotional wellbeing. Psychological follow-up and speech therapy were also provided. After 4 years of follow-up, implant-supported oral rehabilitation has proved to be a satisfactory treatment option, allowing restoration of masticatory, phonetic, and esthetic function, as well as an improvement in the patient's self-esteem and social wellbeing.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

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Implant-supported Oral Rehabilitation in Child with Ectodermal Dysplasia — 4-year Follow-up

Triches

Ximenes

Souza

et al. 2017

Bull. Tokyo Dent. Coll.

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“…1 ED merupakan gangguan yang relatif jarang, dengan frekuensi kejadian bervariasi antara 1:10.000 dan juga 1:100.000 kelahiran hidup dan lebih sering pada laki-laki. 2 Kelainan ED merupakan kelainan herediter yang berbentuk dominan autosomal maupun resesif X-linked. 3 Pada perempuan lebih jarang terjadi karena ketika mutasi gen pada kromosom X yang menyebabkan masalah, biasanya akan jauh lebih jelas pada laki-laki daripada perempuan.…”

Section: Pendahuluanunclassified

Penatalaksanaan Oligodontia pada Anak 14 Tahun dengan Sindrom Ectodermal Dysplasia: Laporan Kasus

Apriani¹,

Sasmita²

2015

mkb

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AbstrakEctodermal dysplasia adalah kelainan herediter yang jarang didapatkan, lebih kurang 7.000 kasus di dunia. Pada kelainan ini terjadi gangguan perkembangan struktur organ-organ yang berasal dari lapisan ektodermal seperti rambut, gigi, kuku, dan kelenjar keringat. Dilaporkan kasus sindrom ectodermal dysplasia pada seorang anak perempuan berusia 14 tahun dengan manifestasi klinis berupa oligodontia (kehilangan gigi lebih dari 6 gigi pada rahang atas dan bawah), rambut tipis dan keriting, abnormalitas bentuk kuku kaki, dan gangguan ekskresi keringat. Tujuan perawatan pasien ini adalah mendapatkan fungsi estetik dan pengunyahan pasien yang terganggu akibat tidak terdapat benih gigi permanen, selain itu juga untuk menjaga supaya pertumbuhan rahang tetap berkembang normal. Penatalaksanaan oligodontia berupa pembuatan gigi tiruan lepasan dan mahkota akrilik pada seluruh gigi anterior rahang atas dan bawah. Simpulan yang didapatkan pada pasien ini adalah tercapainya perbaikan estetika dan pengembalian fungsi pengunyahan serta pemeliharaan pertumbuhan rahang dapat terjaga dengan baik. Ectodermal dysplasia is a hereditary disorder that is rarely seen with approximately 7000 cases in the world. In this disorder, Ectodermal dysplasia occurs as a developmental disorder of organ structures derived from the ectodermal layer such as hair, teeth, nails, and sweat glands. This is a case report of ectodermal dysplasia in a 14-year-old girl with clinical manifestations of oligodontia (tooth loss, more than 6 teeth on the upper and lower jaw), thin and curly hair, abnormal toenail shape, and impaired excretion of sweat. The purpose of the treatment was to make the patient regains her esthetic and masticatory functions, which were disrupted by the absence of permanent tooth buds, as well as to maintain the normal growth of the developing jaws. Treatment for the patient's with oligodontia included the use of removable denture in lower jaw and application of acrylic crowns on all upper and lower anterior teeth resulting in improved esthetics and masticatory function. It is concluded that the treatment has been able to improve the esthetics and to return the masticatory function of the patient while maintaining the normal growth of the jaws. [MKB. 2015;47(4):255-60]

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“…It is a rare, X-linked genetic trait that affects approximately 1 in 10,000 live-born males and 1 in 100,000 live-born females [3,10], at a male to female ratio of 5:1, respectively. Generally, it has phenotypic expression in males and can be genetically inherited from mothers.…”

Section: Introductionmentioning

confidence: 99%

Oral rehabilitation with removable dental prosthesis in a six-year-old patient with hypohidrotic ectodermal dysplasia

Dalledone

Bertoli

Sponchiado

et al. 2017

RSBO

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Introduction: Ectodermal dysplasia is an abnormality of the ectoderm and its derivatives, phenotypically expressed in males and genetically inherited from mothers. Objective: To report the efficacy of the prosthetics treatment of severe ectodermal dysplasia in a 6-year-old boy with hypohidrotic ectodermal dysplasia (HED). Case report: The boy had difficulty in speaking and eating and the condition also affected his self-esteem. Prosthetic treatments included the construction of acrylic custom trays, determination of the vertical dimension of occlusion (VDO), construction of upper and lower dentures, and palatal expansion procedure. Conclusion: Significant improvements in the patient's stomatognathic function and self-esteem were evident.

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Alternative rehabilitation treatment for a patient with ectodermal dysplasia

Cited by 12 publications

References 4 publications

Implant-supported Oral Rehabilitation in Child with Ectodermal Dysplasia — 4-year Follow-up

Implant-supported Oral Rehabilitation in Child with Ectodermal Dysplasia — 4-year Follow-up

Penatalaksanaan Oligodontia pada Anak 14 Tahun dengan Sindrom Ectodermal Dysplasia: Laporan Kasus

Oral rehabilitation with removable dental prosthesis in a six-year-old patient with hypohidrotic ectodermal dysplasia

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