An interesting case of dermatomyositis with classical presentation

Abstract

Dermatomyositis, a connective tissue disorder, is an idiopathic inflammatory myopathy characterised by skin manifestation. The diagnosis of dermatomyositis is based on rashes on the skin, progressive muscle weakness, elevated serum muscle enzymes, abnormal electromyogram, and abnormal findings on muscle biopsy. Hereby presenting this rare case of a 57-year-old female with dermatomyositis with all the typical clinical findings with interstitial lung disease.

A typical case of Dermatomyositis

“…Myositis panel showed Mi2a, Mi2b, RO-52 positive. 3 Based on the above findings of proximal muscle weakness, characteristic rash, elevated CPK, serum LDH, muscle biopsy findings, diagnosis of dermatomyositis was confirmed. She was started on pulse therapy of Methylprednisolone and subsequently shifted to oral maintenance steroid.…”

Unveiling Dermatomyositis: A Tragic Tale of Mortality in a 23-Year-Old

“…In the absence of malignancy, patients with dermatomyositis typically exhibit a favorable prognosis, with five-year survival rates ranging from 70% to 93%. Unfavorable prognostic indicators include advanced age, concomitant interstitial lung disease (ILD), cardiac complications, and delayed or insufficient prior treatment [3].…”