An orbital perivascular epithelioid cell tumor in a 7-year-old boy: case report and review of the literature

Ocular transcription factor E3‐associated perivascular epithelioid cell tumor in children: Case report and review of the literature

“…It is worth noting that including the present case, half [1][2][3][4][5][6][7][8] of the 18 instances with ocular PEComa documented to date were under the age of 18 (Table 1). There are six cases of ocular PEComa and three cases of uveal PEComa.…”

“…The mainstay of treatment for ocular PEComa is surgery. Varan et al 5 found that in a 6-year-old male, who solely underwent systemic chemotherapy, the mass size remained steady over a 6-month period of follow-up.…”

Malignant perivascular epithelioid cell tumor mimicking jugular foramen schwannoma: A case report and literature review

“…PEComas can arise in a variety of anatomic sites. According to our literature review, sites for head and neck PEComas include the nasal cavity [6,7,8,12,14,21,22,25], scalp [5,9,10], neck soft tissue [10], eye [4,11,15,16,19,24,27], oral cavity [14,20], larynx [6,17], pharynx [17,26], face [13], and skull base [18,23]. PEComas arising from sites in the skull base like the jugular foramen are extremely rare.…”

“…The site of origin of this tumor is extremely variable; however, the head and neck are rare origin sites [3,4,5,6,7,8,9,10,11,12,13,14,15,16,17,18,19,20,21,22,23,24,25,26,27], and PEComas arising from the skull base are even more unusual [18,23]. In this report, we describe a case with a PEComa located in the jugular foramen.…”