An unusual example of isolated double-orifice tricuspid valve

Sapre, Ashish; Gopalraj, Sunil S; Kottayil, Brijesh P; Kumar, Raman Krishna

doi:10.4103/0974-2069.115269

Cited by 12 publications

(3 citation statements)

References 4 publications

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“…Most cases are diagnosed incidentally during open-heart surgery or autopsy and it usually coexists with concomitant cardiac anomalies. The occurrence of DOTV is extremely rare and difficult to diagnose by echocardiography; therefore, the condition can be easily overlooked [ 12 – 14 , 31 , 32 ]. The identification of the accessory orifice in the septal leaflet of the tricuspid valve in the present case is compatible with the “hole” variant anomaly described in humans, reflecting the first confirmation of this pathology in a canine patient.…”

Section: Discussionmentioning

confidence: 99%

Canine infantile left ventricular noncompaction

et al. 2020

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Background Left ventricular noncompaction (LVNC) is a rare form of cardiomyopathy currently described in humans and cats. It consists of a spongy myocardium characterized by prominent trabeculation and deep recesses involving more than 50% of the ventricular thickness. We describe the clinical and pathological features of LVNC combined with tricuspid valve dysplasia, double-orifice tricuspid valve and severe pulmonary stenosis in a puppy. In addition, we briefly review the LVNC causes, pathogenesis, forms and current diagnostic criteria. Case presentation A seven-week-old intact German Shorthaired Pointer-cross male was presented with a poor body condition, exercise intolerance and dyspnea. Clinical exam identified a bilateral systolic murmur (grade IV/VI over the right heart base and grade III/VI over the left heart base). Echocardiography identified tricuspid valve dysplasia, mild mitral regurgitation, and severe pulmonic stenosis with a trans-valvar systolic pressure gradient of 106 mmHg. Left ventricular noncompaction was diagnosed by necropsy and further confirmed histopathologically by the presence of two distinct myocardial layers: an inner noncompacted zone covering more than 50% of ventricular thickness containing prominent trabeculation and deep recesses, and an outer zone of compact myocardium. Conclusions This is the first case describing LVNC in a canine patient, supporting the introduction of this form of heart disease as a differential diagnosis for cardiomyopathies in juvenile and adult dogs.

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Section: Discussionmentioning

confidence: 99%

Canine infantile left ventricular noncompaction

et al. 2020

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“…Should the straddling orifice itself be divided in this arrangement, there can seemingly be three atrioventricular valves. [ 17 18 19 20 21 22 ] The presence of the straddling valve is again the consequence of malalignment between the atrial and ventricular septal structures, but with separate atrioventricular junctions rather than a common atrioventricular junction. Depending of the extent of overriding of the straddling valve, there will be variable hypoplasia of one of the ventricles.…”

Section: Discussionmentioning

confidence: 99%

Clarifying the atrioventricular junctional anatomy in the setting of double outlet right atrium

Gupta

Ramakrishnan

et al. 2015

Ann Pediatr Card

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Double outlet atrium is a rare cardiac anomaly wherein one of the atriums, most frequently the right atrium, opens into both the ventricles. Although seen more commonly in the setting of atrioventricular septal defect, this arrangement can also be found when one of the atrioventricular connections is atretic due to absence of the atrioventricular connection and the other atrioventricular valve straddles the muscular ventricular septum. It is the specific anatomy and connections of the atrioventricular junction that clarifies the situation and distinguishes between these two types of double outlet atrium. In this report, we present a case of double outlet right atrium co-existing with the absence of left atrioventricular connection. We then discuss the morphologic aspects of this interesting anomaly.

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“…Double orifice tricuspid valve (DOTV) is an extremely rare malformation first reported by Greenfild. [ 1 ] Each orifice is provided with a fully developed subvalvular tensor apparatus. It can either occur alone or in association with other cardiac malformations, especially with atrio ventricular septal defect (AVSD) as in our case.…”

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confidence: 99%