Anatomic types of single or common ventricle in man

Atresia of the right atrioventricular orifice.

“…Any successful nomenclature should permit accurate description of hearts in all aspects of their anatomy, in particular with regard to the site of atrial orificial atresia and to the ventricular morphology and ventriculoarterial connections. The segmental approach promoted by Van Praagh and his colleagues (Van Praagh et al, 1964;Melhuish and Van Praagh, 1968;Van Praagh, 1972) is ideally suited for this purpose. We have therefore analysed a series of specimens with right atrial orificial atresia using this approach.…”

Anatomically corrected transposition of the great arteries.

“…Cardiac geometry (Van Praagh, Ongley, and Swan, 1964a) showed the following horizontal plane projections relative to the Z axis (the antero-posterior line) in this case (Fig. 1E), compared with the normal (Fig.…”

“…the loop rule (Van Praagh et al, 1964b). Nevertheless, these correlations did prove accurate in 95 per cent of 149 cases of transposition of many types (Van Praagh, Vlad, and Keith, in the press) and in 92 per cent of 60 cases of single ventricle (Van Praagh et al, 1964a). In view of the severe cono-ventricular malalignment which is the essence of anatomically corrected transposition, a segment-by-segment approach to the angiocardiogram appears necessary, assisted by a segmentally deductive approach to the electrocardiogram (Portillo et al, 1959;Sodi-Pallares et al, 1959).…”

Univentricular heart and supravalvular ring

“…Moreover a fibrous ring above the left sided atrioventricular valve was present [1]. This description, supporting by unequivocal images, consists with the classic anatomic form of double inlet left ventricle {S,L,L} [2,3]. In this well known cardiac defect, accordingly with the L-loop of the ventricle, the left atrioventricular valve is not a mitral valve but is a tricuspid valve.…”