Anesthesia for a child with complex I respiratory chain enzyme deficiency

Cheam, E. W. S.; Critchley, Lester A. H.

doi:10.1016/s0952-8180(98)00074-9

Cited by 25 publications

(17 citation statements)

References 15 publications

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“…Cheam et al. (99) also reported satisfactory TIVA administration in a six‐yr‐old child undergoing an orthopedic procedure, a kind of intervention often needed to perform in this group of patients.…”

Section: Total Intravenous Anesthetics and Local Anestheticsmentioning

confidence: 90%

Drug management in emergent liver transplantation of mitochondrial disorder carriers: review of the literature

Vater

Dembo

Martay

et al. 2010

Clinical Transplantation

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Section: Total Intravenous Anesthetics and Local Anestheticsmentioning

confidence: 90%

Drug management in emergent liver transplantation of mitochondrial disorder carriers: review of the literature

Vater

Dembo

Martay

et al. 2010

Clinical Transplantation

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“…An increased risk for malignant hyperthermia has been discussed in several disorders of energy metabolism like CPT2 deficiency [163], respiratory chain defects [164, 165], and McArdle disease [166]. Depolarizing drugs like succinylcholine for muscle relaxation may trigger malignant hyperthermia.…”

Section: Special Problemsmentioning

confidence: 99%

Inborn Errors of Energy Metabolism Associated with Myopathies

Das

Steuerwald

Illsinger

2010

Journal of Biomedicine and Biotechnology

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Inherited neuromuscular disorders affect approximately one in 3,500 children. Structural muscular defects are most common; however functional impairment of skeletal and cardiac muscle in both children and adults may be caused by inborn errors of energy metabolism as well. Patients suffering from metabolic myopathies due to compromised energy metabolism may present with exercise intolerance, muscle pain, reversible or progressive muscle weakness, and myoglobinuria. In this review, the physiology of energy metabolism in muscle is described, followed by the presentation of distinct disorders affecting skeletal and cardiac muscle: glycogen storage diseases types III, V, VII, fatty acid oxidation defects, and respiratory chain defects (i.e., mitochondriopathies). The diagnostic work-up and therapeutic options in these disorders are discussed.

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“…PSA agents such as propofol, narcotics, benzodiazepines, and ketamine all have case reports describing their successful use in children with unusual inborn errors of metabolism. [75][76][77][78][79][80][81][82][83][84] Metabolism or excretion of any sedation or analgesia agent may be prolonged in children with liver or kidney problems. These effects do not impact the initial dosing of a sedative or narcotic, only the timing and amount of subsequent doses.…”

Section: Endocrine/metabolic Problemsmentioning

confidence: 99%

Procedural Sedation for Children With Special Health Care Needs

Sacchetti

Turco²,

Carraccio³

et al. 2003

Pediatric Emergency Care

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Children with special health care needs represent a growing percentage of pediatric patients treated in all emergency departments. Substantial literature exists concerning the medical treatment of these patients, but there is little written describing the management of procedural sedation or analgesia in this population. This article examines the unique anatomic and physiologic implications of procedural sedation or analgesia management in children with special health care needs.

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Anesthesia for a child with complex I respiratory chain enzyme deficiency

Cited by 25 publications

References 15 publications

Drug management in emergent liver transplantation of mitochondrial disorder carriers: review of the literature

Drug management in emergent liver transplantation of mitochondrial disorder carriers: review of the literature

Inborn Errors of Energy Metabolism Associated with Myopathies

Procedural Sedation for Children With Special Health Care Needs

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