Attacks of ventricular fibrillation and unconsciousness in a patient with prolonged QT interval. A family study

Chaudron, J M; Heller, F.; Berghe, H.B. Van den; Lebacq, E

doi:10.1016/s0002-8703(76)80544-3

Cited by 11 publications

(4 citation statements)

References 27 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…For her ventricular arrhythmia, she was initially treated with lidocaine and then with propranolol and digoxin 5. Because of relapsing torsades de pointes, according to Schwartz and colleagues,6 the patient had an extensive stellectomy.…”

Section: Case Reportmentioning

confidence: 99%

Long term follow up of long QT syndrome treated by overdrive pacing

Campanelli

2001

Heart

View full text Add to dashboard Cite

Long term follow up of a patient with idiopathic long QT syndrome is described. A 5 year old girl was admitted with attacks of unconsciousness. Epilepsy was diagnosed and the patient was treated with anticonvulsants. During other episodes, ECG study showed torsades de pointes. The patient was treated with blockers, stellectomy without success, and later with overdrive pacing. The young woman is now 43 years old and in good health. It is suggested that early overdrive pacing be implanted in young people with symptomatic long QT syndrome. (Heart 2001;86:e14)

show abstract

Section: Case Reportmentioning

confidence: 99%

Long term follow up of long QT syndrome treated by overdrive pacing

Campanelli

2001

Heart

View full text Add to dashboard Cite

show abstract

“…Sporadic cases occur but several authors report a clear autosomal dominant pattern for the syndrome without deafness (Gale et al, 1970;Chaudron et al, 1976), while some propose a recessive pattern (Fraser et al, 1964). Mathews et al (1972) reported a family in which the disorder occurred with and without deafness, the latter being inherited separately in a dominant fashion.…”

Section: Nature Of the Diseasementioning

confidence: 99%

“…Phenytoin (Ratshin et al, 1971;Mathews et al, 1972), bretylium tosylate (Singer et al, 1974), digoxin (Chaudron et al, 1976), lignocaine, potassium, and diazepam have all been tried with variable but limited success.…”

Section: Nature Of the Diseasementioning

confidence: 99%

An unusual cause of apparent epilepsy: ECG and EEG findings in a case of Jervell Lange-Neilson syndrome.

Selby¹,

Driver²

1977

Journal of Neurology, Neurosurgery & Psychiatry

View full text Add to dashboard Cite

“…SIDS has been reported in siblings and other close relatives of children with the long QT syndrome (Romano et al, 1963;Fraser and Froggatt, 1964;Chaudron et al, 1976). Fraser and Froggatt (1964) and Schwartz (1976) suggested that some sudden unexpected infant deaths were likely to be associated with this conduction disorder.…”

mentioning

confidence: 99%

Prolonged QT interval and cardiac arrhythmias in two neonates: sudden infant death syndrome in one case.

Southall¹,

Arrowsmith²,

Oakley³

et al. 1979

Archives of Disease in Childhood

View full text Add to dashboard Cite

SUMMARY Two neonates with arrhythmias and the long QT syndrome are described. The arrhythmias were detected in utero and both infants were apparently well after birth. The first infant, although well, had a bradycardia for the first 9 days of life. A normal heart rate was documented at 10 days but a prolonged QT interval was not appreciated on the ECG. He was discharged from hospital but died suddenly and unexpectedly 3 days later. A post-mortem examination failed to find a cause for his death which therefore fell into the category of the sudden infant death syndrome (SIDS). A retrospective analysis of the perinatal electrocardiogram showed a probable junctional rhythm with 2:1 conduction to the ventricle; the QT interval was prolonged at 0 * 52 seconds (QTC = 063). The second infant had a QT interval of 0 * 52 seconds (QTC 0* 54) and frequent ventricular premature beats on a 24-hour electrocardiogram. She was treated with propranolol and remains well 2 years later. Sudden infant death has often been described in the siblings of children with the long QT syndrome and one other report described a case of SIDS which was said to have had a prolonged QT interval on the perinatal ECG. This report, however, provides unquestionable evidence, in one case, of an association between the long QT syndrome and SIDS.

show abstract

Attacks of ventricular fibrillation and unconsciousness in a patient with prolonged QT interval. A family study

Cited by 11 publications

References 27 publications

Long term follow up of long QT syndrome treated by overdrive pacing

Long term follow up of long QT syndrome treated by overdrive pacing

An unusual cause of apparent epilepsy: ECG and EEG findings in a case of Jervell Lange-Neilson syndrome.

Prolonged QT interval and cardiac arrhythmias in two neonates: sudden infant death syndrome in one case.

Contact Info

Product

Resources

About