Bilateral Radial Artery Aneurysms in the Anatomical Snuff Box Seen in Marfan Syndrome Patient: Case Report and Literature Review

Abstract

We describe the first Marfan syndrome case of non-traumatic bilateral radial artery aneurysms in the anatomical snuff box. A 74-year-old woman with Marfan syndrome had a pulsatile mass in her bilateral anatomical snuff box. The color Doppler ultrasonography showed an aneurysm of radial artery located in the bilateral anatomical snuff box. Resection of the right radial artery aneurysm was completed without complications. Histopathological analysis showed a true aneurysm with atherosclerotic changes in the arterial wall. We review the literature on non-traumatic or bilateral radial artery aneurysm in the anatomical snuff box, and discuss the clinical presentation and surgical management.

Extensor pollicis longus tendon compression as the etiology of a true aneurysm of the radial artery in the anatomical snuff box

“…[1][2][3][4][5] One case report attributed a true RAA to repetitive occupational trauma from use of tailor's scissors, 6 and one report described synchronous aneurysms in a patient with Marfan disease. 7 None of the patients presented with symptoms of rupture or embolization.…”

True radial artery aneurysm: A rare cause for finger ischaemia

“…Most radial and ulnar artery aneurysms are traumatic or iatrogenic in origin (e.g., hypothenar hammer syndrome or post‐arterial puncture pseudoaneurysms). A PubMed database search revealed only nine histologically confirmed cases of true degenerative RAAs 1–9 . True RAAs presenting with ischaemic symptoms are exceedingly uncommon with only one previous case reported in the literature 6 …”

“…True aneurysms of the distal radial artery are a rare occurrence, with fewer than 10 confirmed cases reported in the English literature. [1][2][3][4][5][6][7][8][9] Most radial and ulnar artery aneurysms are traumatic or iatrogenic in origin (e.g., hypothenar hammer syndrome or postarterial puncture pseudoaneurysms). A PubMed database search revealed only nine histologically confirmed cases of true degenerative RAAs.…”

“…A PubMed database search revealed only nine histologically confirmed cases of true degenerative RAAs. [1][2][3][4][5][6][7][8][9] True RAAs presenting with ischaemic symptoms are exceedingly uncommon with only one previous case reported in the literature. 6 The patient has consented to the use of his images and case for publication.…”

Atraumatic Left Distal Radial Artery Aneurysm

“…The majority of radial artery aneurysm cases reported in the literature are secondary to a traumatic event, with the anatomical snuffbox being the most common anatomical location [1, 2]. Other upper extremity arterial aneurysm etiologies reported in the literature include mycotic [3], arteriosclerotic [4, 5], idiopathic [6], and underlying vasculopathy [7]. The rarest etiology of radial artery aneurysm is the idiopathic etiology accounting for only nine cases in the literature [8].…”