Bispectral index monitoring in a patient with combination of congenital insensitivity to pain with anhidrosis (CIPA) and Shwachman–Diamond syndrome

Anesthetic Management of Congenital Insensitivity to Pain with Anhidrosis in a Child: A Case Report

“…Generally, patients with CIPA do not require analgesics for the maintenance of anesthesia, and are prone to become hemodynamically unstable with high concentrations of either volatile or intravenous anesthetics. Small doses of sedatives could achieve appropriate anesthetic depth in those patients [6,7]. The anesthetic regimen without opioids could diminish the risk of respiratory depression.…”