Gangliogliomas are rare mixed neuronal-glial tumors of the central nervous system. They constitute less than 2% of intracranial neoplasms. Gangliogliomas are slow-growing, well-differentiated, and partly calci ed tumors. Sellar-suprasellar gangliogliomas are very rare [1]. Although many studies have included only cerebral hemisphere gangliogliomas, the tumor could not be classi ed according to its location because of the small number of patients in most studies [2].Herein, a rare case of a pediatric ganglioglioma in the sellar and parasellar region is presented with a histopathological diagnosis of ganglioglioma from a centre with an annual series of 150 endoscopic skull base surgeries and 900 endoscopic skull base surgeries.