Budd Chiari Syndrome- A Rare Case Report

Abstract

The Budd-Chiari syndrome (BCS) is a rare life threatening and clinically challenging disorder defined by obstruction of hepatic venous outflow anywhere from the small hepatic veins to the suprahepatic inferior vena cava. It is considered as a manifestation of underlying prothrombotic risk factors of which myeloproliferative disorders are the most common ones. We describe a 41year old Male who presented with bilateral lower limb edema and abdominal distension with visible veins over the anterior abdomen which on further evaluation was diagnosed as Budd-chiari syndrome. Budd Chiari syndrome requires a prompt and accurate diagnosis with an aggressive treatment which depends on the cause, clinical presentation and anatomical location of the problem.

Budd chiari syndrome: A case report on a rare disorder

“…Acquired causes include myeloproliferative disorders like polycythemia vera, paroxysmal nocturnal hemoglobinuria, essential thrombocytosis, and myelofibrosis. Other conditions reported as risk factors for the development of BCS include antiphospholipid syndrome, hypereosinophilic syndrome, Behcet disease, and ulcerative colitis [7].…”