Budd‐Chiari Syndrome – Hepatic Venous Outflow Tract Obstruction

Chef, Dominique-Charles Valla Md Professeur

doi:10.1002/9781444393989.ch13

Cited by 7 publications

(17 citation statements)

References 33 publications

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“…Therapeutic options include anticoagulation, thrombolysis, transjugular intrahepatic portosystemic shunt, and LT. ( 272,273 ) Treatment choices in pregnancy are more limited, as vitamin K antagonists are contraindicated in pregnancy due to the risk of fetal hemorrhage and teratogenicity. ( 274,275 ) Thrombolytic therapy may be acceptable, but data are limited.…”

Section: Liver Conditions Requiring Special Management In Pregnancymentioning

confidence: 99%

Reproductive Health and Liver Disease: Practice Guidance by the American Association for the Study of Liver Diseases

et al. 2021

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Section: Liver Conditions Requiring Special Management In Pregnancymentioning

confidence: 99%

Reproductive Health and Liver Disease: Practice Guidance by the American Association for the Study of Liver Diseases

et al. 2021

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“…IVCS may also develop in Budd-Chiari syndrome (BCS), a rare occlusive disease affecting the hepatic veins (HV) and/ or the IVC [14][15][16]. French, Italian, and Swedish studies reported incidences of 0.69 to 2.2 per million inhabitants [17][18][19].…”

Section: Etiology Anatomy and Pathophysiologymentioning

confidence: 99%

“…In Europe, BCS most often occurs in primary and secondary thrombophilia including hormone intake, Behcet's disease, paroxysmal nocturnal hemoglobinuria, and myeloproliferative syndromes [14,16,19,20], whilst in Asia it is often caused by membranous or segmental stenoses or occlusions of the HV and/or the IVC [21]. Rarely, liver tumors or extrahepatic tumors compress or invade the IVC and/or the HV [14][15][16].…”

Section: Etiology Anatomy and Pathophysiologymentioning

confidence: 99%

“…According to the location of the obstruction a truncal type (I) with occlusion of the hepatic segment of the IVC ± HV, a radicular type (II) with occlusion of the hepatic veins, and a veno-occlusive type (III) with obstruction of small centrilobular veins are differentiated [14,15]. Types of IVCinvolvement in BCS have been characterized in more detail as the exact location and extend of these lesions influences interventional strategy.…”

Section: Etiology Anatomy and Pathophysiologymentioning

confidence: 99%

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Inferior vena cava-syndrome

Klein-Weigel

Elitok

Ruttloff

et al. 2021

Vasa

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Summary: Inferior vena cava syndrome (IVCS) is caused by agenesis, compression, invasion, or thrombosis of the IVC, or may be associated with Budd-Chiari syndrome. Its incidence and prevalence are unknown. Benign IVCS is separated from malignant IVCS. Both cover a wide clinical spectrum reaching from asymptomatic to highly symptomatic cases correlated to the underlying cause, the acuity, the extent of the venous obstruction, and the recruitment and development of venous collateral circuits. Imaging is necessary to determine the underlying cause of IVCS and to guide clinical decisions. Interventional therapy has changed the therapeutic approach in symptomatic patients. This article provides an overview over IVCS and focuses on interventional therapeutic methods and results.

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“…Budd-Chiari syndrome is a rare condition, its prevalence being estimated at about 1 case per 100.000 inhabitants, with geographical variations 3,4 . Thus, in some Asian countries, such as Nepal, BCS is considered a relatively common cause of liver disease, while in Western countries it is a rare disease, with an incidence not exceeding 1 case in 2.5 million individuals per year 4 . BCS affects all races and the male-to-female ratio is approximately equal 3 .…”

Section: Epidemiologymentioning

confidence: 99%