Caudal Anesthesia in a Neonate with Dandy-Walker Syndrome

Abstract

Dandy-Walker Syndrome (DWS) is an intrauterine developmental anomaly, which consists of 4-12% of all infants having hydrocephalus its prevalence is 1/30000 in all live births [1,2]. Cranio-facial anomalies such as cleft lip and palate, micrognathia and hypertelorism, together with cardiac and renal anomalies, limb anomalies (syndactyly, polydactyly, etc.) and vertebral anomalies can all be detected in patients with DWS. They may have to undergo a single operation or a series of operations during their childhood period, related to these anomalies. Additionally, these patients may present with features of a difficult airway, together with neurological disorders such as increased intracranial pressure and brain stem dysfunction. All of these situations create numerous serious challenges to the anesthesiologist [3,4]. We were unable to meet any report published in the literature, related to the anesthetic management of patients with DWS until now. We aimed to present our anesthetic management, in a newborn male patient with Dandy-Walker Syndrome, in whom we used caudal block for umbilical cord hernia repair.

Patologías congénitas y defectos del desarrollo en poblaciones arqueológicas en la costa desértica de Antofagasta

“…Esta patología es una anomalía en el desarrollo del sistema nervioso central que puede producirse por una alteración de un gen o de un cromosoma, con una malformación aislada o en conjunto con otras anomalías multifactoriales (Murray et al, 1985). Como rasgos característicos, el síndrome incluye hidrocefalia (1% a 4% de los casos), ausencia parcial o completa del vermis cerebeloso, quiste continuo de la fosa posterior con el cuarto ventrículo (Spennato et al, 2011), deformación en extremidades (polidactilismo y sindactilismo), anomalías craneofaciales (labio leporino y paladar hendido, micrognatia e hipertelorismo), y anomalías cardíacas, renales y vertebrales (Sari et al 2015). Su prevalencia es de uno en 25.0000-30.000 nacimientos y los estudios clínicos muestran una incidencia ligeramente mayor en mujeres (Hirsch et al, 1984;Spennato et al, 2011).…”