Cholesteatoma of the upper urinary tract

Abstract

We report the case of a 57-year old patient with complex cystic image in right kidney. Following radical nephrectomy, the pathological study established the diagnosis of renal cholesteatoma. We discuss the frequency, pathogenesis, clinical presentation, propedeutics, histological findings and proposes for intervention observed in the literature.

Cholesteatoma in ectopic kidney

“…Most often its cystic form is observed. [1] More frequent involvement of the lower urinary system has been also indicated. [3][4][5] It is more frequently seen in adults with a slight male predominancy (male/female: 3/2).…”

“…[1] Firstly it was reported by Rosina in the year 1953. [2] Histopathologically it is characterized with keratinization, and squamous metaplasia of urothelial epithelium associated with desquamation of keratinized layers.…”

Nephron-Sparing Diagnosis and Management of Renal Keratinizing Desquamative Squamous Metaplasia

“…1,[3][4][5][6][7][8][9] The only neoplastic associations in the literature from the past 50 years are from Reece and Koontz, 3 who reported two cases of concurrent renal pelvis KDSM and neoplasm (one transitionalcell carcinoma and one squamous-cell carcinoma). They were unable to provide histologic evidence, however, that the KDSM was involved in the tumor.…”

“…4,7,10 The general appearance of KDSM as a spaceoccupying mass within the kidney prompts consideration of malignancy.…”