Choroid plexus papilloma presenting as an occipital mass with neck pain

Abstract

Rationale:Choroid plexus papillomas are rare benign central nervous system neoplasms arising from choroid plexus epithelium. They are most often located in the lateral ventricle, followed by the fourth and third ventricles and, rarely, in the cerebellopontine angle.Patient concerns:We report an uncommon case of a 17-year-old boy who presented with neck pain that had lasted for more than 1 month, with accompanying pain and numbness in his upper extremities. His conditions included slight dizziness, nausea, diplopia, paresthesia, and an unsteady gait. Magnetic resonance imaging (MRI) showed huge cerebellopontine angle tumor that extended to the front medulla oblongata.Diagnosis:Choroid plexus papilloma (WHO I) was diagnosed in this patient.Interventions:The patient was referred for neurosurgical intervention. The very large neoplasm was subtotally resected.Outcomes:The symptoms of the patient were gradually alleviated after surgery and subsequent radiotherapy treatment, but unfortunately, follow-up of 2 years later revealed that the disease was recurrent and the young man passed away.Lessons:Neck pain is related to many factors. The case provided an awareness of the origin of severe intracranial disease. It is mandatory to take a thorough clinical assessment with a holistic approach.

Extracerebral choroid plexus papilloma in the pharynx with airway obstruction in a newborn: a case report

“…In 2016, the World Health Organization (WHO) classified choroid plexus tumors as CPP (WHO Grade I), atypical CPP (WHO Grade II), and choroid plexus carcinoma (WHO Grade III) [6]. CPPs are wellknown benign neoplasms of the central nervous system, accounting for approximately 0.4-0.6% of all intracranial tumors [7]. Stemming from the neuroectoderm and originating from the choroid plexus lining the ventricles, overproduction of cerebrospinal fluid (CSF) is a critical feature of these tumors [1,2].…”

Extracerebral choroid plexus papilloma in a newborn: a rare presentation

“…CPPs are, theoretically, an important cause of hydrocephalus by increasing the production of cerebrospinal fluid (CSF) and were first reported by Guerard in 1932 in a 3-year-old child 5. CPPs are low-grade rare neoplasms of the central nervous system (CNS), accounting for 0.4%–0.6% of all intracranial CNS neoplasms 6 7. The most common location is the lateral ventricles, but other locations have also been mentioned, including cerebellopontine angle and the third ventricle 1 8 9.…”