Clear cell sarcoma of the abdominal wall with peritoneal sarcomatosis: CT features

Abstract

Clear cell sarcoma, also called malignant melanoma of soft parts, is an uncommon neoplasm that involves tendons or aponeuroses of the lower extremity. The CT features of a clear cell sarcoma arising from the abdominal wall with later peritoneal dissemination are described. Peritoneal sarcomatosis from soft tissue sarcomas is a very rare condition previously unreported in the radiologic literature. Metastases to peritoneal surfaces must therefore be considered a possible site for systemic dissemination of soft tissue sarcomas.

An Osteoclast-Rich Tumor of the Gastrointestinal Tract with Features Resembling Clear Cell Sarcoma of Soft Parts: Reports of 6 Casesof aGIST Simulator

“…A final consideration is that of the entity known as clear cell sarcoma or malignant melanoma of soft parts [8][9][10]. This is a malignant neoplasm usually located in the deep soft tissues (typically in intimate association with tendons or aponeuroses), but which has also been described in the ear, preparotid region [11], abdominal wall [12], chest wall [13], pleura [14], bone [15], skin [16], kidney [17], penis, and gastrointestinal tract (see below). Most patients are between 20 and 40 years of age at the time of diagnosis.…”