The prognosis of patients with initially metastatic ES is very poor. Significant risk factors for death include affectation at combined local and distant sites and soft tissue involvement. For the diagnosis, an initial radiographic and/or computed tomography (CT) is performed. Both techniques are outstanding in evaluating the affected bones. However, when primary Ewing´s tumor or its metastases involves soft tissues, these might be misdiagnosed if magnetic resonance imaging (MRI) is not applied. The purpose of the present case is to expose the role of MRI in the assessment of a rare and aggressive ES with metastases affecting bones and soft tissue of the head.