Congenital constriction ring syndrome of the limbs: A prospective study of 16 cases

Adu, Emmanuel J. K.; Annan, Charles

doi:10.4103/0189-6725.44182

Cited by 13 publications

(11 citation statements)

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“…Dans les pays développés certains auteurs estiment son incidence entre 0,11/10000 [ 5 ] et 1600 naissances [ 1 ]. En Afrique, son incidence n'est pas connue, les cas rapportés proviennent de données hospitalières [ 6 – 8 ]; beaucoup de cas ne sont certainement pas rapportés. Au Burkina Faso, les cas que nous rapportons sont les premiers à notre connaissance alors que les malformations congénitales sont relativement fréquentes en pratique quotidienne.…”

Section: Discussionunclassified

“…Le pronostic du SBA est fonction de la sévérité des malformations. Dans les formes peu sévères, un traitement palliatif chirurgical [ 6 , 11 ] ou prothétique (observations N° 1 et 2) peut permettre au patient d'avoir une qualité de vie optimale. Par contre, le LBWC est au-dessus de toute ressource thérapeutique, le décès est inéluctable soit in utero soit peu après la naissance [ 8 , 15 ], ce que confirme les observations N° 3, 4 et 5.…”

Section: Discussionunclassified

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Le syndrome des brides amniotiques et ses difficultés diagnostiques et de prise en charge au Burkina Faso

Nagalo¹,

Badiel²,

Kouéta³

et al. 2015

Pan Afr Med J

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Le syndrome des brides amniotiques est une embryo-foetopathie rare, d’étiopathogénie encore inconnue, caractérisé par des malformations crânio-faciales, thoraco-abdominales, des membres et des extrémités. Afin de discuter des difficultés diagnostiques et thérapeutiques du syndrome des brides amniotiques, nous rapportons cinq cas de ce syndrome. Ces cas représentaient autant de phénotypes de la maladie mais avec quelques singularités. Les deux premiers étaient des cas de maladie des brides amniotiques caractérisés l'un par une amputation d'un membre inférieur associée à des lésions cutanées et à une surdité, l'autre par des strictions avec amputation des doigts associées à une fente labio-palatine, une cataracte congénitale et un strabisme. Les trois autres cas correspondaient à des formes létales du Limb Body Wall Complex dont deux avec attache placento-crânienne et un avec attache placento-abdominale. Le renforcement du diagnostic anténatal, l'instauration du conseil génétique et la mise en place d'un registre national des malformations devraient permettre d'améliorer la prise en charge des cas du syndrome des brides amniotiques.

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Section: Discussionunclassified

Le syndrome des brides amniotiques et ses difficultés diagnostiques et de prise en charge au Burkina Faso

Nagalo¹,

Badiel²,

Kouéta³

et al. 2015

Pan Afr Med J

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“…12 The syndrome was first described by Montgomery in 1832. [13][14][15][16] ABS comprises a group of anomalies that correspond to 1%-2% of congenital malformations in the general population. 12 ABS prevalence is 1 in 1200 to 15,000 live births.…”

Section: Discussionmentioning

confidence: 99%

“…12 ABS prevalence is 1 in 1200 to 15,000 live births. [12][13][14][17][18][19][20] The male-to-female ratio is 1:1, and it occurs most commonly in the Afro-Caribbean population. 12,15 The syndrome affects both upper and lower extremities at a ratio of 85% 15%, respectively, 16,21 most often involving fingers.…”

Section: Discussionmentioning

confidence: 99%

Amniotic Band Syndrome in Adult Combined with Persistent Depressive Disorder

Kolasiński¹,

Kolenda²,

Kolasinska³

2021

Plastic and Reconstructive Surgery - Global Open

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ongenital amniotic band syndrome (ABS) is an anomaly with no proven etiology occurring in 0.7 per 10,000 live births. 1 This defect mostly concerns the extremities and is often accompanied by other developmental anomalies. 2 There are many methods of treatment for this type of defect. [3][4][5] The literature most often describes cases of treated children. There are no case reports of ABS treatment in adults. However, failure to undertake such treatments in childhood may result in serious mental dysfunction. [6][7][8][9] Here, we present a rare case of ABS in an adult patient and describe our management approach.

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“…2 However, there are 3 theories that are likely to be accepted among hand and plastic surgeons; they are intrinsic theory, 3,8 extrinsic theory, 3 and intrauterine trauma theory. 1,9 The recommended management for the correction of CRS is done in 2 or 3 stages of releasing the constricting ring (Figs. 1 and 2).…”

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confidence: 99%

A Review on the Safety of One-Stage Circumferential Ring Constriction Release

Prasetyono

Sitorus

2015

International Surgery

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The study was undertaken to investigate the use of one-stage circumferential ring-constriction release with Z-plasties regarding the safety, aesthetic appearance, and limb function. A thorough review was conducted on all English publications in PubMed during the period of 2001 through 2011. Titles and abstracts were identified using online search engine from National Library of Medicine's PubMed database under the keywords "limb constriction ring," "limb constriction band," "amniotic band," "annular constriction," and "circumferential constriction." We used Boolean operator and field of title. Evaluation was done to search indications, timing of the first surgical intervention, time interval between surgeries, patients' gender, anatomic location of the ring, wound healing problems, and scar quality. Fourteen publications met the criteria. There were 17 patients with 25 ring constrictions in total. Sixteen ring constrictions (64%) were circumferential; nine (36%) were semi-circumferential. Mean age of 14 patients treated with one-stage release was 4.8 years. Six articles mentioned about normal development of postoperative limb function. Mean age of three patients treated with staged release was 10.5 months. Two articles mentioned regained distal muscle function postoperatively. It is confirmed that surgeons may continue the practice to release circumferential CRS in one stage.

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Congenital constriction ring syndrome of the limbs: A prospective study of 16 cases

Abstract: Congenital constriction ring syndrome is of uncertain aetiology and could cause morbidity in the newborn. The syndrome and its complications are amenable to corrective surgery with good results. Early intervention is desirable for a successful outcome.

Cited by 13 publications

References 1 publication

Le syndrome des brides amniotiques et ses difficultés diagnostiques et de prise en charge au Burkina Faso

Le syndrome des brides amniotiques et ses difficultés diagnostiques et de prise en charge au Burkina Faso

Amniotic Band Syndrome in Adult Combined with Persistent Depressive Disorder

A Review on the Safety of One-Stage Circumferential Ring Constriction Release

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