Congenital Infantile Intracranial Teratoma with Orbital Extension

Abstract

Background: Mature intracranial teratoma in the pediatric population is a rare entity. They are sometimes associated with genetic syndromes but complete surgical excision is associated with good outcome and prognosis. Case Presentation:A 3 months old baby girl presented in the clinic with left eye proptosis, MRI brain showed temporal and retro-orbital multiple cystic lesions, which were excised and biopsy showed mature teratoma. The patient was discharged and followed in the clinic. Conclusion:This case underlies that mature brain teratoma may present at an early age even at birth. They are rare intracranial tumors and may be associated with other genetic syndromes. A high index of suspicion should be present when coming across such complex lesions in neonates. Although the overall outcome of these tumors is generally poor, among the children that survive, complete microsurgical excision of the tumor is associated with good outcome and prognosis. In cases of mature teratomas, we advocate that complete removal should be carried out. In cases of the residual disease, reoperation is indicated to achieve good results.