Congenital Ossification Defects of the Frontal Bone: Description of a Novel Clinical Entity and the Management of Four Patients

Abstract

Embryologic development of the frontoorbital region is complex and is affected by a series of pathologies. These primarily represent failures of fusion at the interface between the frontal bones and the skull base or between the frontal bones themselves, or frontal bone defects in association with atypical craniofacial clefts or cutis aplasia. Isolated ossification defects in the frontal bones themselves are rare, with only 1 case having been previously reported. In that report, the defect was effectively managed with an alloplastic cranioplasty. However, long term results were not presented. Here, we describe 4 cases of isolated frontal bone aplasia their management using autologous bone.

Repair of Congenital Enlarged Parietal Foramina With Porous Polyethylene Implants

“…Enlarged CPFs, although most of them are asymptomatic and diagnosed incidentally either on physical examination or on imaging, 9 some pediatric patients with CPF do indeed have some severe symptoms associated with their defects, including bouts of severe headaches, nausea, vomiting, psychosocial problems, craniosynostosis, craniofacial dysostosis, a syndrome of mental retardation, multiple exostoses, craniofacial dysostosis, and a syndrome of branchial and auricular fistulae with abnormal faces and skeletal deformities 1 . These defects are typically bilateral and symmetric, but they can also present as a single large central opening 1 .…”