Congenital pseudarthrosis of the clavicle is a rare clinical entity, first described in 1910. We report on a 15 year old girl, who presented with a painless lump over mid-portion of right clavicle at her routine newborn examination, which was subsequently diagnosed as a congenital pseudarthrosis when she got into adolescence period. Here we explore its pathogenesis, elaborate on its diagnoses and differential diagnoses in paediatric patients, and comment on its distinct treatment.