Congenital Pseudohorseshoe Lung Associated with Scimitar Syndrome

Abstract

Horseshoe lung is a congenital pulmonary malformation that is usually associated with scimitar syndrome. This malformation consists of fusion of both pulmonary lobes from the posterobasal segments. The fusion appears in the retrocardiac area, in front of the esophagus and thoracic aorta. Pleural separation of pulmonary lobes distinguishes pseudohorseshoe appearance from a true horseshoe lung. Scimitar syndrome known as hypogenetic lung syndrome is a part of the congenital pulmonary venolobar syndrome. It is a partial anomalous pulmonary venous return with pulmonary hypoplasia. Scimitar vein is an anomalous drainage vessel between the right pulmonary lobe vessels and the inferior vena cava. The appearance of the vessel resembles Turkish scimitar; therefore, the syndrome is called scimitar syndrome. We hereby report a 61-year-old woman with adult form congenital scimitar syndrome and will describe the imaging findings of pseudohorseshoe lung appearance.

Hypogenetic right lung with partial anomalous pulmonary venous return and accessory diaphragm: a case of “scimitar lung”

“…The herniated portion may be attached or may be separated by pleural membranes. Pleural separation of pulmonary lobes distinguishes pseudo-horseshoe appearance from a true horseshoe lung [35]. In the case reported here, the fusion of the right and left posterobasal segments were not observed, thus establishing the presence of a pseudo-horseshoe lung (Figure 3).…”

An Unusual Neonatal Presentation of Scimitar Syndrome

“…It has been suggested that when the isthmus is completely encased in a pleural membrane, as it was in our patient, this be termed pseudohorseshoe lung. 8 …”

Imaging spectrum of horseshoe lung: A series of four cases

“…To resolve ambiguity, the authors emphasise the use of only two terms to describe HL on imaging: true HL and pseudo-HL. These can be differentiated by the absence and presence of a pleural fissure between the isthmus and contralateral lung parenchyma in true HL and pseudo-HL respectively, as described previously by Tosun et al 2 …”