Continuous glucose monitoring in children with glycogen storage disease type I

Abstract

CGM could be applied in the clinical setting to help the physician to identify hypoglycemic events, and repeated CGM may serve as a safe and useful tool for the assessment of the long-term management of patients with GSD I.

Lipids in hepatic glycogen storage diseases: pathophysiology, monitoring of dietary management and future directions

“…Continuous glucose monitoring systems are used in GSD patients in the real life situation to improve dietary management and thereby parameters of metabolic control, including the lipid profile (Hershkovitz et al 2001; White and Jones 2011; Kasapkara et al 2014). Nowadays, the most modern (and expensive) devices alarm at low glucose levels, significantly improving safety.…”

“…Reference values for body weight in boys were retrieved from the W orldHealthOrganizationand the Centers for Disease Control and Prevention, below 2 years and after 2 years of age, respectively. EGP was calculated according to Huidekoper (Hershkovitz et al 2001;White and Jones 2011;Kasapkara et al 2014). Nowadays, the most modern (and expensive) devices alarm at low glucose levels, significantly improving safety.…”

Clinical Use of Continuous Glucose Monitoring in Pediatrics

“…The authors conclude that even this timelimited intervention can have meaningful impact for longterm management of patients with GSD I. 45 …”

Alternative nighttime nutrition regimens in glycogen storage disease type I: a controlled crossover study

“…Continuous glucose monitoring systems (CGMS) are now routinely used in outpatient clinics to evaluate and improve glucose control in patients with type 1 diabetes mellitus. CGMS is also sporadically being used by some metabolic centers to assess the quality of glucose control (White and Jones 2011;Kasapkara et al 2014), but has not been used in controlled studies in patients with GSDI.…”