Coronary Sinus Atrial Septal Defect (Unroofed Coronary Sinus) with Total Anomalous Pulmonary Venous Connection—A Case Report

Abstract

Introduction: To present a rare occurrence of coronary sinus atrial septal defect (ASD) associated with total anomalous pulmonary venous connection (TAPVC). Case Report: A 16-year-old girl was diagnosed with features of an atrial septal defect (ASD) by transthoracic echocardiography and the absence of PLSVC (persistent left superior vena cava) connection to coronary sinus was confirmed by saline contrast echocardiography ("bubble study"). Discussion: The cause of the dilated coronary sinus was due to total anomalous pulmonary venous connection. Conclusion: Coronary sinus atrial septal defect (ASD) is a rare interatrial shunt that is commonly associated with a persistent left superior vena cava (PLSVC) and occurs in less than 1% of cases of ASDs. It is characterized by the absence of at least a portion of the common wall that separates the coronary sinus and left atrium. Isolated defects are associated with low rate of morbidity and mortality.

Hypogenetic right lung with partial anomalous pulmonary venous return and accessory diaphragm: a case of “scimitar lung”

“…We speculate that the excessive volume of blood shunted into the right atrium and an increase in intra-atrial pressure associated altered hemodynamics caused the observed widened coronary sinus. In 2017, the coexistence of ASD and 'unroofed coronary sinus' with TAPVC in a 16-year-old female was reported [27]. It seems that dilated coronary sinus is seen in association with ASD [27].…”

“…In 2017, the coexistence of ASD and 'unroofed coronary sinus' with TAPVC in a 16-year-old female was reported [27]. It seems that dilated coronary sinus is seen in association with ASD [27].…”