Cranial Computed Tomographic Scan Appearance of Sturge-Weber Disease: Unusual Presentation

Enzmann, Dieter R.; Hayward, Robert W.; Norman, David; Dunn, Robert P.

doi:10.1148/122.3.721

Cited by 28 publications

(12 citation statements)

References 11 publications

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“…Increasing knowledge about Sturge-Weber disease has yielded evidence that incomplete or atten uated forms, not displaying all features, are not uncommon [3,7,8,13,20], Nowadays it is generally accepted that the absence of the typical facial nevus does not rule out the diagnosis of the Sturge-Weber syndrome pro vided the essential anatomical lesion (namely, the leptomeningeal angio matosis) is present.…”

Section: Discussionmentioning

confidence: 99%

“…Occurrence of bilateral intra cranial calcification is less common, accounting for 17% of reported cases in the literature [4], Also incomplete or atypical cases of this syndrome have been described [3,7,8,15,18], and there is no reason why these should be excluded by definition from the Sturge-Weber syndrome when the basic pathology (namely, leptomeningeal angiomatosis) is present.…”

Section: Introductionmentioning

confidence: 99%

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Sturge-Weber Syndrome without Port-Wine Facial Nevus

Ambrosetto

Michelucci³

et al. 1983

Pediatr Neurosurg

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2 cases of Sturge-Weber syndrome without facial nevus are reported. The patients presented different forms of epilepsy. The diagnosis was made by computed tomography (CT) which showed typical intracranial calcifications in both occipital regions. The problems concerning the atypical and incomplete forms of the syndrome are briefly discussed. The importance of CT as a diagnostic procedure for this disease is emphasized.

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Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Sturge-Weber Syndrome without Port-Wine Facial Nevus

Ambrosetto

Michelucci³

et al. 1983

Pediatr Neurosurg

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“…Enzmann el at. [6] described this finding in their 3 cases with this disease. However, in the presence of minimal calci fication, cortical atrophy may not be seen, as illustrated by case 1.…”

Section: Discussionmentioning

confidence: 78%

Computed Tomography of Sturge-Weber Disease

Maki¹,

Semba²

1979

Pediatr Neurosurg

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Findings in computed tomography (CT) with or without contrast infusion were analyzed in 8 patients with Sturge-Weber disease. From the extent of calcification in the CT, Sturge-Weber disease can be classified into two types, localized and diffuse. The extent of calcification or cortical atrophy is predictable, if it can be shown that enhanced areas in contrast infusion CT truly represent leptomeningeal angiomatos¡s. Thus, using enhanced CT, the capacity of prediction as to whether the patient will have a localized or diffuse type of disease will be possible with further observations.

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“…Sturge-Weber Sendromlu olgularda tedaviye dirençli konvülziyon varlığında serebral lobektomi veya hemisferektomi operasyonları planlanması ya da sıkça görülen glokom nedeni ile genel anestezi uygulanması zorunlu olabilir (6,7). Anestezi uygulamalarından önce yandaş anomalileri saptayabilmek için dikkatli bir inceleme şarttır.…”

Section: Discussionunclassified

“…Sunulan olguda peroperatif ve postoperatif analjezi sağlamak amacıyla kaudal blok uygulandı ve rejyonel anestezinin planlandığı alanda hemanjiomlar olabileceği düşüncesi ile kaudal anestezi USG eşliğinde başarıyla gerçekleştirildi. Sonuç olark; SWS'li olgularda intrakraniyal ve intraoküler basıncı artırabilecek her türlü girişimden kaçınılmalı, hemanjiyomlar travmadan korunmalı ve eşlik eden diğer bulgular ve gelişebilecek komplikasyonlar için önlemler alınmalıdır (6,7,8). Çocuk olgularda ultrason eşliğinde kaudal anestezinin güvenle uygulanabileceği kanısındayız.…”

Section: Discussionunclassified

Sturge-Weber Sendromlu Olguda Anestezi Yonetimi

2018

GMJ

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ÖZETSturge-Weber Sendromu sporadik olarak ortaya çıkan, konjenital gelişen, nörokutanöz bir hastalıktır. Bu hastalıkta leptomeningeal hemanjiom, trigeminal sinir bölgesine dağılmış genellikle tek taraflı Porto şarabı nevus, oküler anomali (glokom) görülür. Hemanjiomların yerleşimi ve büyüklüğü, intraoküler ve intrakaranyal basıncın korunması anestezi uygulamalarında özel dikkat gerektirir. Bu yazıda genel anestezi altında sağ spermatik kord kisti eksizyonu ve sünnet planlanan 4 yaşındaki erkek olguda anestezi yönetimi sunularak literatür bilgileri ışığında tartışılması hedeflenmiştir. ABSTRACT Sturge-Weber Syndrome is a sporadic, congenital, neuro-cutaneous disease. In this disease, leptomeningeal hemangioma, the unilateral Port wine nevus that distributed in the trigeminal nerve region and ocular anomaly (glaucoma) is usually seen. The placement and size of hemangiomas requires special attention in the practice of anesthesia for the protection of intraocular and intracranial pressures. In this article, we aimed to present anesthesia management under general anesthesia in the case of 4-year-old male who planned the right spermatic cord cyst excision plus circumcision and discussion in the light of literature information.

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Cranial Computed Tomographic Scan Appearance of Sturge-Weber Disease: Unusual Presentation

Cited by 28 publications

References 11 publications

Sturge-Weber Syndrome without Port-Wine Facial Nevus

Sturge-Weber Syndrome without Port-Wine Facial Nevus

Computed Tomography of Sturge-Weber Disease

Sturge-Weber Sendromlu Olguda Anestezi Yonetimi

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