Cystic intraventricular schwannoma: case report and review of the literature

Abstract

Intraventricular schwannoma is an exceedingly rare tumour with only 6 cases described in the literature. One case of a cystic intraventricular schwannoma operated on at our Institution is analyzed and the other cases reported in the literature are reviewed. Complete removal was achieved and no recurrence was noted after a follow-up period of 10 years. Intraventricular schwannomas are rare tumours that are amenable to complete surgical removal, having a good prognosis without the need of adjuvant therapy.

Intracerebral schwannomas: a rare disease with varying natural history

“…28,31 There appears to be no sex predilection in cases of intracerebral schwannoma. 4,5 The first report of these tumors was published in 1966. 23 It described the case of a temporal lobe schwannoma in a 6-year-old boy with a 1-year history of seizure disorder.…”

Fourth Ventricular Schwannoma: Identical Clinicopathologic Features as Schwann Cell-Derived Schwannoma with Unique Etiopathologic Origins

“…Intraventricular schwannomas are very rare tumors with only 17 previously reported cases in the literature [1–16] (see Table 1). The vast majority of reported cases have been located in the lateral ventricle with only 5 cases in the fourth ventricle [6, 12, 15, 16].…”

“…Based on the previously reported literature, this neoplasm appears to assume a benign course with no recurrence when there is no histological evidence of malignancy. Barbosa et al described a case of cystic intraventricular schwannoma without recurrence for 10 years after resection [1]. Of the two reported cases of malignant intraventricular schwannomas, one was identified incidentally during autopsy [10] while the other patient had recurrence with drop metastases requiring reoperation and whole brain radiation [8].…”

“…Intraventricular schwannomas are rare tumors with only 17 cases reported in the literature [1–16]. The etiology of intraventricular schwannomas is not known but they are thought to arise from a separate mechanism from the commonly encountered intracranial schwannomas.…”

Supratentorial intraventricular schwannoma of the choroid plexus

“…A variety of intraventricular tumours can be found, with the differential diagnosis depending upon the location in the ventricular system [2][3][4] . In the lateral ventricles, the more common intraventricular tumours are meningiomas, astrocytomas and ependymomas, whereas choroid plexus papillomas and carcinomas, subependymomas and dermoid cysts are rare 3,5 .…”