Diagnostic features and pitfalls in the two-dimensional echocardiographic evaluation of a child with cor triatriatum

Abstract

Two-dimensional echocardiography has been successfully used to diagnose cor triatriatum in adults and children, and surgical referral of these patients has been undertaken without preceding cardiac catheterization and angiography. A child with cor triatriatum demonstrated by two-dimensional echocardiography was directly referred for surgical resection. Despite thorough preoperative echocardiographic examination and direct intraoperative inspection of the posterior left atrial chamber, partial anomalous right pulmonary venous drainage was not diagnosed until the postoperative period. The failure to detect this uncommon associated anomaly underscores the limitations of relying on two-dimensional echocardiography as the sole preoperative method of evaluation.

Severe Pulmonary Hypertension Caused by Cor triatriatum sinistrum: Diagnosis and Assessment of Severity with Two-Dimensional Doppler Echocardiography

“…The most important thing in this case is the capability of two-dimensional echocardiography to de tect the intra-atrial membrane of the cor triatriatum as a possible cause of the pulmonary hypertension. This case so far confirms earlier reports on the usefulness of twodimensional echocardiography in the diagnosis of this malformation [1][2][3][4][5][6]. The severity of the obstruction can…”

Cor triatriatum associated with partial anomalous pulmonary venous connection to the coronary sinus: Echocardiographic and angiocardiographic features

“…The elevated pressure in the proximal left atrial chamber contributes to retention of some primitive channels arising from the cardinal or umbilicovitelline systems [15]. In patients with cor triatriatum who have PAPVC, involvement of the left pulmonary veins is more common [17], which contrasts with the usual pattern of isolated PAPVC in which the right pulmonary veins are involved ten times more frequently than the left [13]. The coexistence of PAPVC with cot triatriatum is suggested by detecting lobar or unilateral variation in pulmonary congestion on a chest radiograph [2] or pulmonary wedge pressures at catheterization [2], features present in our patient.…”

“…Previous reports have described direct anastomosis of pulmonary veins to the right atrium [7,15] or drainage to the superior vena cava either directly [7,17] or via the vertical and innominate veins [2,7,9,16]. The diagnosis of PAPVC associated with cor triatriatum can be difficult and even missed at surgery [17] and has not been made previously by echocardiography. In this report, we describe a patient with cor triatriatum and a new associated variety of PAPVC, namely, drainage of the left pulmonary veins to the coronary sinus.…”

Anesthetic Management of 70 Year Old Woman with Cor triatriatum Sinister

“…Cor Triatriatum is a rare congenital abnormality consisting 0.1-0.4% of congenital heart disease [1]. CT results from the division of the atrium into a proximal and distal chamber.…”