Diffuse Thoracic Lymphangiomatosis With Disseminated Intravascular Coagulation in a Child

Tamay, Zeynep; Sarıbeyoğlu, Ebru; Öneş, Ülker; Anak, Sema; Güler, Nermin; Bılgıç, Bilge; Yılmazbayhan, Dilek; Gün, Feryal

doi:10.1097/01.mph.0000193476.14493.06

Cited by 25 publications

(20 citation statements)

References 20 publications

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“…Tamay et al reported the case of an 8-year old girl with diffuse lymphangiomatosis and disseminated intravascular coagulation. 4 The hemoptysis in this patient was mainly the result of a bleeding tendency.…”

Section: Discussionmentioning

confidence: 97%

Invasive Lymphangioma of the Lung Manifesting as a Large Pulmonary Mass with Hemoptysis: Report of a Case

et al. 2007

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Solitary lymphangioma of the lung is rare. We report a case of invasive lymphangioma of the lung, diagnosed in a 9-year-old girl who presented with intractable hemoptysis and a large pulmonary mass, 10 cm in diameter. We performed left lower lobectomy and lingular segmentectomy to remove the mass completely and the patient has been well for 3 years since. Pathologically, the mass was partly polycystic and partly solid. Irregular and dilated vascular and lymphatic vessels, as well as fibrosis of the interstitium, were spreading into the adjacent lung parenchyma, demonstrating their invasive nature. A new monoclonal antibody, D2-40, which reacts with lymphatic endothelium, proved useful for establishing the pathological diagnosis. We suggest that these pathological findings might be consistent with the intermediate type of localized lymphangioma of the lung and diffuse lymphangiomatosis.

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Section: Discussionmentioning

confidence: 97%

Invasive Lymphangioma of the Lung Manifesting as a Large Pulmonary Mass with Hemoptysis: Report of a Case

et al. 2007

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“…The aetiology of the haemorrhage in these cases is not wellknown but it can be related with the infiltrative proliferation of lymph vessels or with coagulation problems as disseminated intravascular coagulation [16,17].…”

Section: Sirmentioning

confidence: 99%

Diffuse lymphangiomatous hyperplasia of the spleen with hyaline bodies. A pseudotumoral proliferation arising from the lymphatic vessels of the periarteriolar lymphatic sheath

et al. 2011

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“…In a minority of cases, consumption coagulopathy is also observed. [1][2][3][4][5] This report describes the rare case of thoracic lymphangiomatosis with a massive chylothorax in a patient after undergoing a tumor biopsy, which also demonstrated disseminated intravenous coagulation (DIC).…”

Section: Introductionmentioning

confidence: 94%

Thoracic lymphangiomatosis with massive chylothorax after a tumor biopsy and with disseminated intravenous coagulation — lymphoscintigraphy, an alternative minimally invasive imaging technique: Report of a case

et al. 2011

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Thoracic lymphangiomatosis in childhood is a rare disorder that frequently has poor response to medical therapy as well as a poor prognosis. This disease is often misdiagnosed, and a defi nitive diagnosis is usually delayed because of the rarity and slow course of the disease. No previous reports have so far described the usefulness of lymphoscintigraphy in the diagnosis of lymphangiomatosis, although some authors have reported the effi cacy of lymphoscintigraphy for evaluating chylothorax. A 6-year-old boy presented with a diffuse mediastinal mass and received an open mediastinal biopsy for a defi nitive diagnosis, which led to the occurrence of massive chylothorax postoperatively. A diagnosis of lymphangiomatosis was fi nally made based on the lymphoscintigraphic fi ndings demonstrating an obstruction of the thoracic duct. This report describes a rare case of thoracic lymphangiomatosis diagnosed at autopsy, and suggests that the minimally invasive technique of lymphoscintigraphy should be employed to obtain a defi nitive diagnosis at an early stage.

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Diffuse Thoracic Lymphangiomatosis With Disseminated Intravascular Coagulation in a Child

Cited by 25 publications

References 20 publications

Invasive Lymphangioma of the Lung Manifesting as a Large Pulmonary Mass with Hemoptysis: Report of a Case

Invasive Lymphangioma of the Lung Manifesting as a Large Pulmonary Mass with Hemoptysis: Report of a Case

Diffuse lymphangiomatous hyperplasia of the spleen with hyaline bodies. A pseudotumoral proliferation arising from the lymphatic vessels of the periarteriolar lymphatic sheath

Thoracic lymphangiomatosis with massive chylothorax after a tumor biopsy and with disseminated intravenous coagulation — lymphoscintigraphy, an alternative minimally invasive imaging technique: Report of a case

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