Double chambered right ventricle in a patient with hypertrophic cardiomyopathy. A unique coexistence

Tyczyński, Paweł; Śpiewak, Mateusz; Chmielewski, Przemysław; Kotliński, Krzysztof; Deptuch, Tomasz; Witkowski, Adam; Szymański, Piotr

doi:10.33963/kp.a2021.0023

Cited by 1 publication

(1 citation statement)

References 4 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…However, DCRV complicated by HCM is an extremely rare coexistence. Several cases reported this unique condition complicated with HCM (2,5,6). With respect to the combination of arrhythmias, Alvarez et al reported that, in two adult patients diagnosed with DCRV, complicated by sustained monomorphic ventricular tachycardia, tachycardia did not reoccur after surgical excision of the abnormal muscle bundles (7).…”

Section: Discussionmentioning

confidence: 99%

Case report: Double-chambered right ventricle diagnosed in a middle-aged female with hypertrophic cardiomyopathy and atrial flutter: A rare case

Liu

et al. 2022

Front. Cardiovasc. Med.

View full text Add to dashboard Cite

Double-chambered right ventricle (DCRV) is a rare congenital heart defect in adults, manifesting with progressive right ventricular outflow tract obstruction. We describe the first case of DCRV coexisting with hypertrophic cardiomyopathy, which is complicated by atrial flutter. A middle-aged woman with recurrent symptomatic atrial flutter who had previously been diagnosed with biventricular hypertrophic cardiomyopathy was admitted to our department. Echocardiography and cardiac magnetic resonance revealed asymmetrical interventricular septal hypertrophy, and abnormal muscle bundles within the right ventricle, generating an obstructive gradient. Genetic testing detected a hypertrophic cardiomyopathy-associated mutation: MYH7, c.4135G > A, p. Ala1379Thr. A diagnosis of DCRV complicated by hypertrophic cardiomyopathy and atrial flutter was made. Surgical intervention was performed, which included radiofrequency ablation, removal of abnormal muscle bundles, and ventricular septal defect repair. Intraoperative transesophageal echocardiography demonstrated the well-corrected right ventricular outflow tract. Free of early postoperative complications, the patient was discharged in sinus rhythm on the 11th day after the surgery. Unfortunately, the patient died from a sudden death 38 days following the surgery. In conclusion, the coexistence of DCRV with hypertrophic cardiomyopathy in patients is an uncommon condition. The present case highlights the importance of diagnostic imaging in the management of this disorder.

show abstract

Section: Discussionmentioning

confidence: 99%

Case report: Double-chambered right ventricle diagnosed in a middle-aged female with hypertrophic cardiomyopathy and atrial flutter: A rare case

Liu

et al. 2022

Front. Cardiovasc. Med.

View full text Add to dashboard Cite

show abstract

Double chambered right ventricle in a patient with hypertrophic cardiomyopathy. A unique coexistence

Cited by 1 publication

References 4 publications

Case report: Double-chambered right ventricle diagnosed in a middle-aged female with hypertrophic cardiomyopathy and atrial flutter: A rare case

Case report: Double-chambered right ventricle diagnosed in a middle-aged female with hypertrophic cardiomyopathy and atrial flutter: A rare case

Contact Info

Product

Resources

About