Dyke-Davidoff-Masson Syndrome: A Delayed Diagnosis of an Acquired Variant

Kumar, T Seetam; Vipul, Abhijit; Yadav, Rohitash

doi:10.15419/jmri.121

Cited by 3 publications

(3 citation statements)

References 9 publications

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“…In cases of intractable disabling seizures, hemispherectomy is an available neurosurgical option and has reported an 85% success rate. Long-term management includes physiotherapy for hemiparesis, occupational therapy, speech therapy for speech defects, psychiatric counseling, and medications if required [1,16].…”

Section: Discussionmentioning

confidence: 99%

Dyke-Davidoff-Masson Syndrome: A Case Report

Chunchu¹,

Kommalapati²,

Pemma³

et al. 2023

Cureus

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Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological entity that is predominantly seen in childhood. Here, we present the case of a 13-year-old girl who was brought to the pediatric ward for general examination with a previous history of seizures, speech difficulty, facial deviation, and progressive leftsided hemiparesis that started at the age of two, followed by delayed developmental milestones. Computed tomography (CT) and magnetic resonance imaging (MRI) of the brain showed right cerebral hemiatrophy, ventriculomegaly, hyperpneumatization of the sinus, the decreased caliber of cortical veins, and skull thickening on the right were all characteristic findings of DDMS. Based on the history, clinical presentation, and imaging findings from CT and MRI, DDMS was confirmed. Identifying DDMS in a clinical setting can be challenging because of low awareness of the condition and varied clinical presentations. Although CT and MRI imaging are the gold standards in diagnosing DDMS, the early manifestations of the disease cannot be well-appreciated on a CT and would likely require an MRI. Since there is no standardized protocol for managing DDMS, the treatment is primarily symptomatic. Early identification and diagnosis of the syndrome are essential to aid the child's mental and physical development through a multidisciplinary approach. There is also a need to improve awareness of DDMS so that the condition can be considered a potential differential diagnosis amongst other similar conditions and does not get misdiagnosed. The lack of a proper protocol for the management of DDMS prompts more research for a better understanding and early identification of the condition.

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Section: Discussionmentioning

confidence: 99%

Dyke-Davidoff-Masson Syndrome: A Case Report

Chunchu¹,

Kommalapati²,

Pemma³

et al. 2023

Cureus

View full text Add to dashboard Cite

show abstract

Section: Discussionmentioning

confidence: 99%

“…3 Acquired DDMS occurs later in life after birth and might be caused by trauma, vascular abnormalities, hemorrhages, aortic coarctation, subependymal germinal matrix, intraventricular hemorrhage in premature infants, and amniotic bands. 4 In their article, "Dyke-Davidoff-Masson syndrome: a case report," Rashid et al 5 provide a case report. In this case, a 13-year-old was suffering from episodes of focal impaired awareness seizures that were accompanied by headaches.…”

Section: Therapeutic Intervention Follow-up and Outcomementioning

confidence: 99%