Early localized morphea mimicking an acquired port-wine stain

Nijhawan, Rajiv I.; Bard, Susan; Blyumin, Marianna L.; Smidt, Aimee C.; Chamlin, Sarah L.; Connelly, Elizabeth Alvarez

doi:10.1016/j.jaad.2009.10.017

Cited by 27 publications

(16 citation statements)

References 13 publications

(10 reference statements)

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“…16 An incorrect diagnosis of acquired portwine stain can be mistaken in cases of early morphea ( Table 2). 24 TREATMENT Morphea lesions tend to regress spontaneously over 3 to 5 years, often leaving residual pigmentary or atrophic changes. 15,18 Therefore, treatment should be focused on treating active areas of involvement, characterized by a violaceous or erythematous margin.…”

Section: Differential Diagnosismentioning

confidence: 99%

Pediatric Morphea

Browning

2013

Dermatologic Clinics

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This article outlines the epidemiology, pathogenesis, clinical presentation, diagnosis, and treatment of childhood morphea. Also known as localized scleroderma, morphea is a fibrosing disorder of the skin and subcutaneous tissues. Morphea is differentiated from systemic sclerosis (scleroderma) based on the absence of sclerodactyly, Raynaud phenomenon, and nail-fold capillary changes. Confusion may occur because patients with morphea often have systemic symptoms such as malaise, fatigue, arthralgias, myalgias, and positive autoantibodies. Unlike morphea, systemic sclerosis has organ involvement, particularly gastrointestinal, pulmonary, and renal.

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Section: Differential Diagnosismentioning

confidence: 99%

Pediatric Morphea

Browning

2013

Dermatologic Clinics

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“…In a retrospective analysis of 136 patients with localized scleroderma, Christen-Zaech et al (6) found one patient with lichen striatus at the same site of subsequent development of linear morphea. Linear morphea has previously been reported to coexist with or precede other entities such as lichen sclerosus (7), port-wine stain (8), granuloma anular (9), and systematized morphea (10). In one patient, linear morphea has been linked to two other conditions, nevus comedonicus, and lichen striatus (11).…”

Section: Discussionmentioning

confidence: 97%

Linear Morphea Mimicking Lichen Striatus in Its Early Presentation

Muñoz-Garza

Mercadè

Crespo

et al. 2015

Pediatric Dermatology

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“…30 In some cases, skin biopsies may be required to establish a diagnosis. 31 Other important differential diagnoses in pediatrics include pilomatricoma, which is characterized by a superficial mobile hard mass with bluish discoloration and an irregular surface. 32 Finally, kaposiform hemangioendotheliomas are indurated, ill-defined vascular tumors with a pebbly surface that may regress spontaneously, leaving a persistent cutaneous stain.…”

Section: Discussionmentioning

confidence: 99%

Dermatofibrosarcoma Protuberans in Pediatric Patients

Rios

Lara‐Corrales

2014

J Cutan Med Surg

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Background: Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue tumor. In children, there are acquired and congenital presentations. Due to clinical similarities with other conditions, diagnosis may be delayed.Objective: To review the clinical characteristics and treatment of DFSP in pediatric patients. Methods: A retrospective chart review was performed from January 2002 to September 2012. Inclusion criteria were patients under 18 years of age with a histopathologic diagnosis of DFSP. Data on demographics, clinical characteristics, treatments, and outcomes were collected.Results: Information was gathered from 17 patients; 9 (53%) were female. Congenital lesions were reported in 7 patients. The mean delay of diagnosis was 5.7 years; the most common anatomic location was the trunk in 8 of 17 (47%) cases. Treatment options included wide local surgery, Mohs surgery, and imatinib mesylate. Conclusion: A detailed medical history and identification of the natural course of common conditions seen in pediatric patients are important to identify less common lesions and to suspect DFSP. Contexte: Le dermatofibrosarcome (DFS) de Darier et Ferrand est une tumeur peu fré quente des tissus mous. Il existe des formes acquises et des formes congé nitales chez les enfants. La pose du diagnostic peut ê tre retardé e en raison de ressemblances cliniques avec d'autres affections. Objectif: L'é tude visait à passer en revue les caracté ristiques cliniques du DFS et de son traitement chez les enfants. Mé thode: Nous avons procé dé à un examen ré trospectif de dossiers mé dicaux, couvrant la pé riode de janvier 2002 à septembre 2012. Les critè res de sé lection comprenaient un â ge infé rieur à 18 ans et un diagnostic histopathologique de DFS. Ont é galement é té recueillies des donné es dé mographiques ainsi que des donné es sur les caracté ristiques cliniques, les traitements, et les ré sultats cliniques.Ré sultats: Les renseignements recueillis provenaient de 17 patients, dont 9 (53%) é taient de sexe fé minin. Des lé sions congé nitales ont é té relevé es chez 7 patients. Le temps moyen é coulé avant la pose du diagnostic é tait de 5.7 ans, et le siè ge le plus fré quent des lé sions é tait le tronc, dans 8 cas sur 17 (47%). Les traitements comprenaient la chirurgie locale é largie, la chirurgie de Mohs, et le traitement par le mé sylate d'imatinib.Conclusion: Une anamnè se dé taillé e et la reconnaissance de l'é volution naturelle d'affections fré quentes observé es chez les enfants sont des é lé ments importants de l'identification de lé sions moins fré quentes et de la pré sence pré sumé e du DFS.

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Early localized morphea mimicking an acquired port-wine stain

Cited by 27 publications

References 13 publications

Pediatric Morphea

Pediatric Morphea

Linear Morphea Mimicking Lichen Striatus in Its Early Presentation

Dermatofibrosarcoma Protuberans in Pediatric Patients

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