Syringoma is a benign neoplasm originating from the eccrine ducts of the sweat gland. Lesions are most commonly located on the face. Rarely, do syringomas develop in the vulvar region, where they may be accompanied by persistent pruritus. The article presents the case of a 34-year-old female patient, in whom small nodules and pruritus of the vulva had persisted for approximately two years. The paper includes a description of the dermoscopic features of the skin lesions. The final diagnosis was made based on the histopathological examination. The paper also discusses the most used therapeutic methods in this rare entity.