Endometriosis is a unique entity described in the extensive literature as the decidualization of endometrial tissues under the influence of gynecologic hormones outside the uterine cavity; Estrogen-dependent endocrine-gynecological pathology, common in women in the fertile period or menopause, a unique entity described as the presence of endometrial tissue in extrauterine sites; Cutaneous endometriosis is rare, and accounts for about 5% of reports of extrapelvic endometriosis, localizing mainly in the umbilicus region. To identify scientific findings on the diagnosis and clinical management of this rare clinical entity. Integrative review used in this article aims to review methods, theories and/or empirical studies on a topic; For the construction, six steps were outlined and included articles published in the last 10 running years. Cutaneous endometriosis is a rare condition in which endometrial tissue grows outside the uterus. Diagnosis is challenging, but symptoms such as pain and swelling in the umbilicus may be indicative. Dermatoscopy and biopsy are helpful in diagnosis. Treatment can be surgical or hormonal, with surgical excision being the preferred option. Recurrence is low after complete excision. Prognosis is generally favorable with appropriate surgery. Cutaneous endometriosis can affect quality of life and fertility, but many women are able to become pregnant after surgical treatment. Preventive measures include care during cesarean section surgery. Cutaneous endometriosis is a rare and difficult to diagnose disease. Treatment involves surgical resection with clear margins. The lack of scientific studies makes clinical management difficult, but summarizing the best evidence can help in early identification and prevention of complications.