Epidermolysis Bullosa Pruriginosa Associated with Folliculitis Decalvans: Case Report and Review of the Literature

Machado, Maria Cecília Rivitti; Toma, Juliana Takiguti; Pompeu, Vivianne Martins Almeida; Valente, Neusa Yuriko Sakai; Doche, Isabella

doi:10.1159/000485521

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2022

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“…Although FD seems frequent in patients with DEB, no cases have been published, with the exception of one patient with DEB pruriginosa and FD 4 . Blistering of the scalp involving the lamina lucida and the rest of the basement membrane zone (BMZ) situated beneath, as in the junctional and dystrophic forms of EB, can lead to cicatricial alopecia secondary to the inflammatory process and chronic wounds 5 .…”

Section: Figurementioning

confidence: 99%

Folliculitis decalvans and dystrophic epidermolysis bullosa: a significant association

Matard

Bourrat

Cavalié

et al. 2022

British Journal of Dermatology

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This work reports 30 cases of folliculitis decalvans (FD) in patients with dystrophic epidermolysis bullosa (DEB) among a cohort of 125 DEB patients seen between 2010 and 2021 in 2 French expert centers for the management of inherited epidermolysis bullosa. Such an association between two rare diseases cannot be fortuitous and implies a physiopathological link that we discuss in this paper. This association is a new significant fact to add to the reflexion on FD causes, suggesting that skin abnormality of DEB could act as a factor of a specific skin barrier alteration which could favor FD. Scarring alopecia with tufted folliculitis and pustules on inflamed skin at the vertex of a woman with dominant dystrophic epidermolysis bullosa.

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Section: Figurementioning

confidence: 99%