Epithelioid haemangioendothelioma

Epithelioid hemangioendothelioma of the liver

“…Liver transplantation has been performed successfully in patients with severe hepatic dysfunction. 5,8,19,89 In our series, liver transplantation was performed in 7 patients; 2 patients died 4 and 62 months, respectively, after surgery, whereas the other 5 patients were alive at a range of 30 months-10 years from the diagnosis. A total of 35 cases treated by orthotopic hepatic transplantation have been reported in the literature.…”

“…5 Hepatic EHE also has been confused with venoocclusive disease because of its tendency to invade terminal hepatic venules 6,9 and to present clinically as the Budd-Chiari syndrome. 6,8,9,19,22 Identification of dendritic and/or epithelioid cells positive for endothelial cell markers and the invasive growth pattern will confirm the neoplastic nature of the occlusive venous lesions. 9,40 …”

Indications for referral and assessment in adultliver transplantation: a clinical guideline

“…Histological assessment is notoriously difficult and misleading, with this tumour on occasion resembling a chronic Budd-Chiari syndrome/veno-occlusive disease,101 or cholangiocarcinoma. Factor VIII related antigen staining and arteriography are often required in diagnostic assessment.…”

Scintigraphic Imaging of Hepatic Epithelioid Hemangioendothelioma

“…However, since 1982 -when Weisse and Enzinger [1] characterized this neoplasm -more case reports and studies on histochemical and radiological findings and specific treatment of EHE have been reported [12][13][14][15]. Therefore, it is becoming more and more important to find an easy, economic, and noninvasive method to diag nose EHE and follow up these patients.…”