Erythromelanosis follicularis faciei et colli: Dermoscopy and dermatopathology correlates

Abstract

A 17-year-old Moroccan boy, without medical history or similar cases in the family, presented with a 3-year history of nonitchy erythemato-pigmented patches, surmounted by follicular papules, on both cheeks, without lesions of keratosis pilaris on the body (Fig 1).

Dermoscopy as a Noninvasive Diagnostic Modality in Erythromelanosis Follicularis Faciei et Colli: A Case Series

“…Errichetti et al for the first time and our findings were consistent with their study [6]. Mouni et al [7] later on revealed similar findings in their patients. Similar dermoscopic findings can be seen in erythrosis pigmentosa peribuccalis which is considered to be a variant of this disease by few authors [8].…”

“…The findings on dermoscopy of follicular plugging, scaling, and reddish brown background correspond to histopathological findings of hyperkeratotic hair follicles, orthokeratosis, and ectatic vessels respectively. Gray-blue dots and granules correlate with the presence of pigmentary incontinence and dermal melanophages in the upper dermis respectively [6,7].…”

Dermoscopy of acquired pigmentary disorders: a comprehensive review

“…On dermoscopy, EFFC presents with white scaling, follicular plugging, and several grey-blue dots interspersed over an erythematous-brown background. 26,27 This corresponds to orthokeratosis, follicular hyperkeratosis, pigment incontinence with dermal melanophages, and vasodilation on histology, respectively. 27 The grey-blue granules, as described by Errichetti et al and Maouni et al, are "peppered" around and inbetween follicular openings.…”

Co-existent erythromelanosis follicularis faciei et colli and erythroses pigmentosa mediofacialis in a patient of generalized keratosis pilaris - A rare report in a young female

“…Dermoscopy of EFFC shows multiple round whitish areas with follicular plugs, some shows central hair, surrounded by blue gray spots or peppering in a reddish-brown background. [ 8 ] Dermoscopy of EPM includes follicular dilatation with yellowish keratotic plugs, perifollicular erythema, and scaling surrounded by slate-gray globules. [ 9 ] Histology of EFFC and EPM is similar and shows follicular hyperkeratosis, increased basal layer pigmentation, and incontinence of melanin pigment with dermal melanophages.…”

“…Dermis shows perivascular and periadnexal lymphocytic infiltrate with vasodilatation. [ 8 ] EFFC has been found to be associated with keratosis pilaris of different body parts which postulated that EFFC is a variant of keratosis pilaris. [ 3 4 6 7 10 11 ] Juhlin et al .…”