Familial Complete Atrioventricular Block (FCAVB) DDDR Pacemaker Implant with Synchromax

Abstract

We present the case of a family with complete atrioventricular block involving several generations, with autosomal dominant Mendelian inheritance, where one of those long-term affected presents heart failure. This entity corresponds to progressive familial heart block type I, mainly described in South Africa. Permanent Pacemaker implant using Synchromax was successful.