No abstract

Acquired long QT syndrome (aLQTS) can occur in up to one third of patients undergoing cardiac surgery and is often undisclosed. We present a case of a 55-year-old male patient admitted to our center for mitral valve replacement surgery, and, during the postoperative period, a long QT greater than 600 ms was confirmed and in the Holter monitoring Torsade de Pointes (TdP) was evidenced. The patient received appropriate medical treatment and was discharge in stable clinical conditions.

We present the case of a family with complete atrioventricular block involving several generations, with autosomal dominant Mendelian inheritance, where one of those long-term affected presents heart failure. This entity corresponds to progressive familial heart block type I, mainly described in South Africa. Permanent Pacemaker implant using Synchromax was successful.