Prenatal midgut volvulus is difficult to diagnose, and it is particularly difficult to evaluate the degree of rotation, which may be related to prognosis. We present a rare case of prenatal midgut volvulus with a 720 rotation around the superior mesenteric artery diagnosed based on ultrasonography, and jejunal atresia was noted at the same time. This condition was supported by prenatal magnetic resonance imaging and the subsequent postnatal operation. To the best of our knowledge, there is no previous literature describing similar ultrasound findings in the prenatal period. Recognition of the color Doppler ultrasound imaging findings can help elucidate the relationship among the twisted vessels of midgut volvulus during the prenatal examination.