Fibrosarcoma congénito de pared torácica

Fibrosarcome infantile simulant un hémangiome type rapidly involuting congenital hemangioma (RICH)

“…La cytogénétique permet de confirmer le diagnostic en mettant en évidence la translocation spécifique du fibrosarcome congénital infantile (ETV6/NTRK3) [8]. Le traitement consiste classiquement en l'exérèse chirurgicale complète avec souvent une amputation [10] associée à une chimiothérapie. Cette nécessité d'une exérèse large, donc d'une amputation dans le cas présenté, a été discutée lors de plusieurs réunions multidisciplinaires et il a été conclu que l'amputation pouvait être évitée.…”

Congenital fibrosarcoma of the chest wall: Report of a case

“…Very few of them are congenital fibrosarcoma (CFS). [1] CFS is the soft tissue sarcoma (STS) of which only 60 cases are documented as congenital. [23] Thus, because of rarity of cases and lack of clinical experience, diagnosis and treatment are challenging.…”

“…Distal extremities are the usual location of involvement. [145] The chest wall has been mentioned as the location for CFS only rarely. [1] Prognosis of CFS of the chest wall is poorer when compared to CFS of distal extremities.…”

“…[145] The chest wall has been mentioned as the location for CFS only rarely. [1] Prognosis of CFS of the chest wall is poorer when compared to CFS of distal extremities. [16] Here, we report a case of a large CFS of the chest wall.…”

“…[1] Prognosis of CFS of the chest wall is poorer when compared to CFS of distal extremities. [16] Here, we report a case of a large CFS of the chest wall.…”