Fibrous Dysplasia of the Frontal Sinus

Rojas, Rafael; Palacios, Enrique; Kaplan, Javier; Wong, Lisa Kim

doi:10.1177/014556130408300107

Cited by 15 publications

(11 citation statements)

References 3 publications

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“…Patients with the monostotic form are frequently asymptomatic and are often diagnosed incidentally during radiographic evaluation for another purpose. Conversely, patients with the polyostotic form have early manifestations including bone pain and/or bone deformity . FD may be associated with other syndromes such as McCune–Albright (precocious puberty, FD, and cutaneous pigmentation–cafe au lait spots) .…”

Section: Benign Lesionsmentioning

confidence: 99%

ICAR: endoscopic skull‐base surgery

Wang

Zanation

Gardner

et al. 2019

Int Forum Allergy Rhinol

160

279

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Background Endoscopic skull‐base surgery (ESBS) is employed in the management of diverse skull‐base pathologies. Paralleling the increased utilization of ESBS, the literature in this field has expanded rapidly. However, the rarity of these diseases, the inherent challenges of surgical studies, and the continued learning curve in ESBS have resulted in significant variability in the quality of the literature. To consolidate and critically appraise the available literature, experts in skull‐base surgery have produced the International Consensus Statement on Endoscopic Skull‐Base Surgery (ICAR:ESBS). Methods Using previously described methodology, topics spanning the breadth of ESBS were identified and assigned a literature review, evidence‐based review or evidence‐based review with recommendations format. Subsequently, each topic was written and then reviewed by skull‐base surgeons in both neurosurgery and otolaryngology. Following this iterative review process, the ICAR:ESBS document was synthesized and reviewed by all authors for consensus. Results The ICAR:ESBS document addresses the role of ESBS in primary cerebrospinal fluid (CSF) rhinorrhea, intradural tumors, benign skull‐base and orbital pathology, sinonasal malignancies, and clival lesions. Additionally, specific challenges in ESBS including endoscopic reconstruction and complication management were evaluated. Conclusion A critical review of the literature in ESBS demonstrates at least the equivalency of ESBS with alternative approaches in pathologies such as CSF rhinorrhea and pituitary adenoma as well as improved reconstructive techniques in reducing CSF leaks. Evidence‐based recommendations are limited in other pathologies and these significant knowledge gaps call upon the skull‐base community to embrace these opportunities and collaboratively address these shortcomings.

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Section: Benign Lesionsmentioning

confidence: 99%

ICAR: endoscopic skull‐base surgery

Wang

Zanation

Gardner

et al. 2019

Int Forum Allergy Rhinol

160

279

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“…The association of other expansile lesions such as a mucocele or ABC with sinus FD may result in rapid growth of the combined lesion [61,62]. This is particularly concerning in areas adjacent to the skull base and brain such as the sphenoid, ethmoid, and frontal sinuses where access may be limited.…”

Section: Sinusesmentioning

confidence: 99%

Clinical guidelines for the management of craniofacial fibrous dysplasia

Fitzgibbon

et al. 2012

Orphanet Journal of Rare Diseases

238

296

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Fibrous dysplasia (FD) is a non-malignant condition caused by post-zygotic, activating mutations of the GNAS gene that results in inhibition of the differentiation and proliferation of bone-forming stromal cells and leads to the replacement of normal bone and marrow by fibrous tissue and woven bone. The phenotype is variable and may be isolated to a single skeletal site or multiple sites and sometimes is associated with extraskeletal manifestations in the skin and/or endocrine organs (McCune-Albright syndrome). The clinical behavior and progression of FD may also vary, thereby making the management of this condition difficult with few established clinical guidelines. This paper provides a clinically-focused comprehensive description of craniofacial FD, its natural progression, the components of the diagnostic evaluation and the multi-disciplinary management, and considerations for future research.

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“…When the disease processes become complicated induced by the increased orbital and intracranial pressure, patients may present with visual disturbance and proptosis, even neurological symptoms, including headache, facial pain, cranial nerve palsy, convulsion, seizure, and meningitis [11][12][13][14] .…”

Section: Discussionmentioning

confidence: 99%